WEGENER GRANULOMATOSIS PRESENTING WITH SCLEROKERATITIS DIAGNOSED BY ANTINEUTROPHIL CYTOPLASMIC AUTOANTIBODIES (ANCA)

被引:10
作者
FLORINE, CW [1 ]
DWYER, M [1 ]
HOLLAND, EJ [1 ]
机构
[1] BEMIDJI CLIN,BEMIDJI,MN
关键词
ANTINEUTROPHIL CYTOPLASMIC AUTOANTIBODIES; SCLERITIS; WEGENER GRANULOMATOSIS;
D O I
10.1016/0039-6257(93)90067-H
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
A 23-year-old male presented with bilateral sclerokeratitis. He reported recent bronchitis, sinusitis, dyspnea on exertion, hemoptysis, arthralgias and myalgias. Wegener's granulomatosis was diagnosed by a positive antineutrophil cytoplasmic autoantibody (ANCA) test and a nasal and subglotic biopsy showing granulomatous inflammation. Treatment with cyclophosphamide, systemic corticosteroids and trimethoprim/sulfamethoxazole resulted in resolution of the sclerokeratitis and remission of the disease.
引用
收藏
页码:373 / 376
页数:4
相关论文
共 9 条
[1]  
BULLEN CL, 1983, OPHTHALMOLOGY, V90, P279
[2]   INTERPRETATION OF HEAD AND NECK BIOPSIES IN WEGENERS GRANULOMATOSIS - A PATHOLOGICAL-STUDY OF 126 BIOPSIES IN 70 PATIENTS [J].
DEVANEY, KO ;
TRAVIS, WD ;
HOFFMAN, G ;
LEAVITT, R ;
LEBOVICS, R ;
FAUCI, AS .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1990, 14 (06) :555-564
[3]  
DUNCKER G, 1990, APMIS S19, V98, P22
[4]   WEGENERS GRANULOMATOSIS, SYSTEMIC VASCULITIS, AND ANTINEUTROPHIL CYTOPLASMIC AUTOANTIBODIES [J].
FALK, RJ ;
JENNETTE, JC .
ANNUAL REVIEW OF MEDICINE, 1991, 42 :459-469
[5]   WEGENERS GRANULOMATOSIS - PROSPECTIVE CLINICAL AND THERAPEUTIC EXPERIENCE WITH 85 PATIENTS FOR 21 YEARS [J].
FAUCI, AS ;
HAYNES, BF ;
KATZ, P ;
WOLFF, SM .
ANNALS OF INTERNAL MEDICINE, 1983, 98 (01) :76-85
[6]   OCULAR MANIFESTATIONS OF WEGENERS GRANULOMATOSIS - 15 YEARS EXPERIENCE AND REVIEW OF LITERATURE [J].
HAYNES, BF ;
FISHMAN, ML ;
FAUCI, AS ;
WOLFF, SM .
AMERICAN JOURNAL OF MEDICINE, 1977, 63 (01) :131-141
[7]   ANTINEUTROPHIL CYTOPLASMIC AUTOANTIBODIES AND ASSOCIATED DISEASES - A REVIEW [J].
JENNETTE, JC ;
FALK, RJ .
AMERICAN JOURNAL OF KIDNEY DISEASES, 1990, 15 (06) :517-529
[8]  
SOUKIASIAN SH, 1992, OPHTHALMOLOGY, V99, P125
[9]  
WATSON PG, 1980, OPHTHALMOLOGY, V87, P716