PRIMARY HYPEROXALURIA - ROENTGENOGRAPHIC CLINICAL AND PATHOLOGIC FINDINGS

被引:9
作者
WEBER, AL
机构
来源
AMERICAN JOURNAL OF ROENTGENOLOGY RADIUM THERAPY AND NUCLEAR MEDICINE | 1967年 / 100卷 / 01期
关键词
D O I
10.2214/ajr.100.1.155
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
The case histories of 6 children with primary hyperoxaluria*'' and the associated roentgenographic findings are presented. This disorder is characterized by increased urinary excretion of oxalic and glycolic acids with formation of urinary tract stones and/or nephrocalcinosis. The disease is most likely inherited as a recessive autosomal trait. The symptoms are related to the urinary tract, and death, usually the result of uremia, often occurs in childhood or early adult life. Roentgen studies demonstrate stones in the urinary tract or nephrocalcinosis with associated pyelonephritis.
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页码:155 / +
页数:1
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