FUCHS ENDOTHELIAL DYSTROPHY OF THE CORNEA

被引:231
作者
ADAMIS, AP
FILATOV, V
TRIPATHI, BJ
TRIPATHI, RC
机构
[1] YALE UNIV, SCH MED, DEPT OPHTHALMOL & VISUAL SCI, NEW HAVEN, CT 06510 USA
[2] UNIV CHICAGO, PRITZKER SCH MED, DEPT OPHTHALMOL & VISUAL SCI, CHICAGO, IL 60637 USA
关键词
CORNEAL EDEMA; CORNEAL ENDOTHELIUM; CORNEAL TRANSPLANTATION; DESCEMET MEMBRANE; FUCHS DYSTROPHY; GROWTH FACTORS; GUTTAE;
D O I
10.1016/0039-6257(93)90099-S
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
Fuchs' endothelial dystrophy of the cornea is a significant cause of corneal blindness in the United States. The disease is characterized by a slow, continuous loss of morphologically and physiologically altered endothelial cells, eventually leading to corneal edema. The endothelial cells synthesize a thickened Descemet's membrane with focal excrescences of altered basement membrane material (guttae). This review details the epidemiological, clinical, and laboratory data that have accumulated on Fuchs' dystrophy. Several hypotheses regarding the pathogenesis of Fuchs' dystrophy are discussed, including the possible influences of aberrent embryogenesis, hormones, and injury on the development of the disease. The current state of medical and surgical management is summarized, along with the future prospects for treatment.
引用
收藏
页码:149 / 168
页数:20
相关论文
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