DEFECTIVE PROTEIN-FOLDING AS A CAUSE OF DISEASE

被引：46

作者：

SIFERS, RN ^{[1
]}

机构：

[1] BAYLOR COLL MED, DEPT CELL BIOL, HOUSTON, TX 77030 USA

来源：

NATURE STRUCTURAL BIOLOGY | 1995年 / 2卷 / 05期

关键词：

D O I：

10.1038/nsb0595-355

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

A defined, spontaneous protein folding defect can act as a common link between lung and liver diseases associated with the Z type of plasma alpha 1-antitrypsin deficiency.

引用

页码：355 / 357

页数：3

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