PHENYLKETONURIA - CLINICAL AND EXPERIMENTAL CONSIDERATIONS REVEALED BY THE USE OF ANIMAL-MODELS

被引:16
作者
LANE, JD
NEUHOFF, V
机构
关键词
D O I
10.1007/BF01054531
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:227 / 233
页数:7
相关论文
共 65 条
[1]   NEURONAL LESIONS IN CEREBELLUM FOLLOWING ADMINISTRATION OF EXCESS PHENYLALANINE TO NEONATAL RATS [J].
ADELMAN, LS ;
MANN, JD ;
CALEY, DW ;
BASS, NH .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1973, 32 (03) :380-393
[2]  
ALTHAUS HH, 1977, H-S Z PHYSIOL CHEM, V358, P1155
[3]  
ALTHAUS HH, 1978, ABS SOC NEUR, V4, P311
[4]   ENDURING BEHAVIORAL CHANGES IN RATS WITH EXPERIMENTAL PHENYLKETONURIA [J].
ANDERSEN, AE ;
GUROFF, G .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (04) :863-&
[5]   ENDURING BEHAVIORAL-CHANGES IN RATS WITH EXPERIMENTAL PHENYLKETONURIA [J].
ANDERSEN, AE ;
ROWE, V ;
GUROFF, G .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1974, 71 (01) :21-25
[6]  
[Anonymous], 1967, CEREBELLUM NEURONAL, DOI 10.1007/978-3-662-13147-3
[7]   BRAIN UPTAKE AND PROTEIN INCORPORATION OF AMINO-ACIDS STUDIED IN RATS SUBJECTED TO PROLONGED HYPERPHENYLALANINEMIA [J].
ANTONAS, KN ;
COULSON, WF .
JOURNAL OF NEUROCHEMISTRY, 1975, 25 (03) :309-314
[8]   HYPERPHENYLALANINEMIA - DISAGGREGATION OF BRAIN POLYRIBOSOMES IN YOUNG RATS [J].
AOKI, K ;
SIEGEL, FL .
SCIENCE, 1970, 168 (3927) :129-&
[9]   EFFECT OF PHENYLALANINE METABOLITES ON ACTIVITIES OF ENZYMES OF KETONE-BODY UTILIZATION IN BRAIN OF SUCKLING RATS [J].
BENAVIDES, J ;
GIMENEZ, C ;
VALDIVIESO, F ;
MAYOR, F .
BIOCHEMICAL JOURNAL, 1976, 160 (02) :217-222
[10]  
BICKEL H, 1972, PHENYLKETONURIA