CHRONIC POLIOENCEPHALITIS WITH CEREBRAL ATROPHY IN INFANTILE X-LINKED HYPOGAMMAGLOBULINEMIA

被引:4
作者
LIWNICZ, BH [1 ]
MARINKOVICH, VA [1 ]
机构
[1] STANFORD UNIV,SCH MED,DEPT PATHOL NEUROPATHOL,STANFORD,CA 94305
关键词
D O I
10.1136/jnnp.42.4.357
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The development of a chronic polioencephalitis is reported in a patient with infantile X-linked hypogammaglobulinaemia (IXH, Bruton type agammaglobulinaemia). In early childhood, the patient had multiple episodes of purulent inflammation involving the meninges and respiratory tract. He was given continuous administration of gammaglobulin and intermittent treatment with antibiotics, and survived for 21 yr. The neuropathological lesion, which revealed severe cerebral atrophy, is described.
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页码:357 / 362
页数:6
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