SARCOMA OF THE PULMONARY-ARTERY - REPORT OF 2 CASES AND A REVIEW OF THE LITERATURE

被引:23
作者
RAMP, U
GERHARZ, CD
IVERSEN, S
SCHWEDEN, F
STEPPLING, H
GABBERT, HE
机构
[1] UNIV MAINZ,DEPT CARDIOVASC SURG,W-6500 MAINZ,GERMANY
[2] UNIV MAINZ,DEPT RADIOL,W-6500 MAINZ,GERMANY
[3] UNIV MAINZ,DEPT INTERNAL MED,W-6500 MAINZ,GERMANY
关键词
PULMONARY ARTERY SARCOMA; HISTOMORPHOLOGY; CLINICAL ASPECTS;
D O I
10.1007/BF01225272
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Primary tumours of the pulmonary arteries are rare neoplasms seldom diagnosed during the patient's life time. We report on two cases of pulmonary artery sarcomas diagnosed during life time of the respective patients in intra-operative frozen sections by histopathological examination. Case 1 was of a 55-year-old man with a fibrosarcoma originating from the main pulmonary trunk. Case 2 was of a 43-year-old woman with a malignant fibrous histiocytoma originating from the right pulmonary artery. In both patients a radical tumour resection under cardiopulmonary bypass was attempted. Both patients, however, had a local tumour recurrence and died 18 months (patient 1) and 6 months (patient 2) after surgery. A review of pulmonary artery sarcomas is given.
引用
收藏
页码:551 / 556
页数:6
相关论文
共 34 条
[1]  
ALTMAN NH, 1973, JOHNS HOPKINS MED J, V133, P214
[2]  
BAKER PB, 1985, ARCH PATHOL LAB MED, V109, P35
[3]   ANTE MORTEM DIAGNOSIS OF PRIMARY LEIOMYOSARCOMA OF THE PULMONARY-ARTERY [J].
BALDUIN, R ;
DRIGO, R ;
SCHIRALDI, C ;
CARRARO, R .
RESPIRATION, 1986, 49 (04) :307-310
[4]  
BLEISCH VR, 1980, CANCER, V46, P314, DOI 10.1002/1097-0142(19800715)46:2<314::AID-CNCR2820460217>3.0.CO
[5]  
2-T
[6]   PRIMARY SARCOMA OF MAIN PULMONARY ARTERY [J].
CAIN, H .
DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 1969, 94 (32) :1607-+
[7]  
DIGILIO M M, 1972, Chest, V62, P639
[8]  
Eisenmann B, 1977, Ann Chir Thorac Cardiovasc, V16, P315
[9]  
ELPHINSTONE R, 1951, THORAX, V14, P333
[10]   PRIMARY PULMONARY-ARTERY SARCOMA IN 2 CHILDREN [J].
FAROOKI, ZQ ;
CHANG, CH ;
JACKSON, WL ;
CLAPP, SK ;
HAKIMI, M ;
ARCINIEGAS, E ;
PINSKY, WW .
PEDIATRIC CARDIOLOGY, 1988, 9 (04) :243-251