DOWLING-DEGOS DISEASE, HIDRADENITIS SUPPURATIVA, AND MULTIPLE KERATOACANTHOMAS - A DISORDER THAT MAY BE CAUSED BY A SINGLE UNDERLYING DEFECT IN PILOSEBACEOUS EPITHELIAL PROLIFERATION

被引:40
作者
FENSKE, NA
GROOVER, CE
LOBER, CW
ESPINOZA, CG
机构
[1] UNIV S FLORIDA,COLL MED,DIV DERMATOL & CUTANEOUS SURG,TAMPA,FL 33612
[2] JAMES A HALEY VET HOSP,DERMATOL SECT,TAMPA,FL
[3] JAMES A HALEY VET HOSP,LAB SERV,TAMPA,FL
关键词
D O I
10.1016/0190-9622(91)70141-N
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We report a case in which one patient had Dowling-Degos disease (reticulate pigmented anomaly of the flexures), hidradenitis suppurativa, and multiple keratoacanthomas. Abnormal epithelial proliferation involving mainly the pilosebaceous apparatus has been recognized in all three conditions. We speculate that a single underlying defect in follicular epithelial proliferation, characterized by variable expressivity, accounts for the coexistence of these clinically distinct disorders of follicular derivation.
引用
收藏
页码:888 / 892
页数:5
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