3-METHYLCROTONYLGLYCINE EXCRETION IN 3-HYDROXY-3-METHYLGLUTARIC ACIDURIA

被引:16
作者
WYSOCKI, SJ
HAHNEL, R
机构
关键词
D O I
10.1016/0009-8981(78)90464-3
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
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页码:101 / 108
页数:8
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共 16 条
[1]   QUANTITATIVE EXTRACTION AND GAS-LIQUID CHROMATOGRAPHIC DETERMINATION OF ORGANIC ACIDS IN URINE [J].
CHALMERS, RA .
ANALYST, 1972, 97 (1161) :958-967
[2]  
ELDJARN L, 1970, LANCET, V2, P521
[3]   URINARY ORGANIC-ACID PROFILE ASSOCIATED WITH 3-HYDROXY-3-METHYLGLUTARIC ACIDURIA [J].
FAULL, KF ;
BOLTON, PD ;
HALPERN, B ;
HAMMOND, J ;
DANKS, DM .
CLINICA CHIMICA ACTA, 1976, 73 (03) :553-559
[4]   MASSIVE EXCRETION OF 2-OXOGLUTARIC ACID AND 3-HYDROXYISOVALERIC ACID IN A PATIENT WITH A DEFICIENCY OF 3-METHYLCROTONYL-COA CARBOXYLASE [J].
FINNIE, MDA ;
COTTRALL, K ;
SEAKINS, JWT ;
SNEDDEN, W .
CLINICA CHIMICA ACTA, 1976, 73 (03) :513-519
[5]  
GOMPERTZ D, 1971, LANCET, V2, P22
[6]  
GOMPERTZ D, 1972, 9TH P S SOC STUD INB, P38
[7]   ACCUMULATION OF 3-HYDROXYISOBUTYRIC ACID, 2-METHYL-3-HYDROXYBUTYRIC ACID AND 3-HYDROXYISOVALERIC ACID IN KETOACIDOSIS [J].
LANDAAS, S .
CLINICA CHIMICA ACTA, 1975, 64 (02) :143-154
[8]   GAS CHROMATOGRAPHY MASS SPECTROMETRY STUDIES OF HIPPURIC ACID DERIVATIVES .1. EVALUATION OF METHODS FOR QUANTITATIVE-DETERMINATION OF HIPPURIC ACID - SEARCH FOR BENZOYLSARCOSINE EXCRETION IN NORMAL URINE [J].
LANGENBECK, U ;
SEEGMILLER, JE .
JOURNAL OF CHROMATOGRAPHY, 1973, 80 (01) :81-88
[9]   IDENTIFICATION OF N-ACYLGLYCINES BY GAS-LIQUID-CHROMATOGRAPHY [J].
ONEILLROWLEY, B ;
GERRITSEN, T .
CLINICA CHIMICA ACTA, 1975, 62 (01) :13-19
[10]   GAS-CHROMATOGRAPHIC STUDIES OF 20 METABOLICALLY IMPORTANT ACYLGLYCINES [J].
RAMSDELL, HS ;
TANAKA, K .
CLINICA CHIMICA ACTA, 1977, 74 (02) :109-114