TREATMENT OF A JAPANESE PATIENT WITH FAMILIAL AMYLOIDOTIC POLYNEUROPATHY WITH ORTHOTOPIC LIVER-TRANSPLANTATION

被引：11

作者：

ANDO, Y

TASHIMA, K

TANAKA, Y

NAKAZATO, M

ERICZON, BG

DURAJ, FF

SAKASHITA, N

KIMURA, E

ANDO, E

YONEHARA, T

YAMASHITA, T

NAKAMURA, M

UCHINO, M

ANDO, M

机构：

[1] Department of Internal Medicine, Miyazaki Medical College, Miyazaki

[2] Department of Internal Medicine, Kumamoto University School of Medicine, Kumamoto 860

[3] Department of Transplantation Surgery, Huddinge Hospital

[4] Department of Opthalmology, Kumamoto University School of Medicine, Kumamoto

来源：

INTERNAL MEDICINE | 1994年 / 33卷 / 11期

关键词：

AMYLOIDOSIS; TRANSTHYRETIN; JAPANESE PATIENT; HEART-BEATING CADAVERIC DONOR;

D O I：

10.2169/internalmedicine.33.730

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 28-year-old male patient with familial amyloidotic polyneuropathy (FAP) underwent a liver transplantation from a heart-beating cadaveric donor in Sweden. He had suffered from the disease for 2.5 years. It took 5.5 hours to carry out the operation without blood transfusion. After the liver transplantation, serum amyloidgenic variant transthyretin (TTR) levels became extremely low and dirrhea stopped after the 7th day. On day 13, the patient was discharged from the hospital and one month after the transplantation, his general condition remained quite good. This is the first case of a Japanese patient with congenital metabolic disorders as well as FAP to receive a liver transplantation from a heart-beating cadaveric donor.

引用

页码：730 / 732

页数：3

共 13 条

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