INCREASED CONCENTRATIONS OF CHOLESTANOL AND APOLIPOPROTEIN-B IN THE CEREBROSPINAL-FLUID OF PATIENTS WITH CEREBROTENDINOUS XANTHOMATOSIS - EFFECT OF CHENODEOXYCHOLIC ACID

被引:81
作者
SALEN, G
BERGINER, V
SHORE, V
HORAK, I
HORAK, E
TINT, GS
SHEFER, S
机构
[1] UNIV MED & DENT NEW JERSEY,NEW JERSEY MED SCH,DEPT MED,NEWARK,NJ 07103
[2] SOROKA MED CTR,DEPT NEUROL,IL-84101 BEERSHEBA,ISRAEL
[3] BEN GURION UNIV NEGEV,FAC HLTH SCI,BEERSHEBA,ISRAEL
[4] UNIV CALIF LAWRENCE LIVERMORE NATL LAB,DIV BIOMED SCI,LIVERMORE,CA 94550
关键词
D O I
10.1056/NEJM198705143162002
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1233 / 1238
页数:6
相关论文
共 37 条
  • [1] COMPUTED-TOMOGRAPHY IN CEREBROTENDINOUS XANTHOMATOSIS
    BERGINER, VM
    BERGINER, J
    SALEN, G
    SHEFER, S
    ZIMMERMAN, RD
    [J]. NEUROLOGY, 1981, 31 (11) : 1463 - 1465
  • [2] EEG IN CEREBROTENDINOUS XANTHOMATOSIS (CTX)
    BERGINER, VM
    RADWAN, H
    KORCZYN, AD
    KOTT, E
    SALEN, G
    SHEFER, S
    [J]. CLINICAL ELECTROENCEPHALOGRAPHY, 1982, 13 (02): : 89 - 96
  • [3] LONG-TERM TREATMENT OF CEREBROTENDINOUS XANTHOMATOSIS WITH CHENODEOXYCHOLIC ACID
    BERGINER, VM
    SALEN, G
    SHEFER, S
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1984, 311 (26) : 1649 - 1652
  • [4] BRADBURY MWB, 1984, FED PROC, V43, P186
  • [5] TISSUE-SPECIFIC EXPRESSION AND DEVELOPMENTAL REGULATION OF THE RAT APOLIPOPROTEIN-B GENE
    DEMMER, LA
    LEVIN, MS
    ELOVSON, J
    REUBEN, MA
    LUSIS, AJ
    GORDON, JI
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1986, 83 (21) : 8102 - 8106
  • [6] Engvall E, 1980, Methods Enzymol, V70, P419
  • [7] HOSHITA T, 1980, J LIPID RES, V21, P1015
  • [8] HUMAN APOLIPOPROTEIN-B CDNA CLONE ISOLATION AND DEMONSTRATION THAT LIVER APOLIPOPROTEIN-B MESSENGER-RNA IS 22 KILOBASES IN LENGTH
    HUANG, LS
    BOCK, SC
    FEINSTEIN, SI
    BRESLOW, JL
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1985, 82 (20) : 6825 - 6829
  • [9] ILLINGWORTH D R, 1970, Biochimica et Biophysica Acta, V220, P610, DOI 10.1016/0005-2744(70)90292-5
  • [10] ISHIGURO S, 1986, J BIOCHEM-TOKYO, V99, P1081