HEMOGLOBIN SAVERNE - A NEW VARIANT WITH ELONGATED BETA-CHAINS - STRUCTURAL AND FUNCTIONAL-PROPERTIES

被引:21
作者
DELANOEGARIN, J
BLOUQUIT, Y
AROUS, N
KISTER, J
POYART, C
NORTH, ML
BARDAKDJIAN, J
LACOMBE, C
ROSA, J
GALACTEROS, F
机构
[1] HOP BICETRE,INSERM,U299,F-94275 KREMLIN BICETRE,FRANCE
[2] CTR TRANSFUS SANGUINE,F-67000 STRASBOURG,FRANCE
关键词
D O I
10.3109/03630268808998034
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:337 / 352
页数:16
相关论文
共 33 条
[1]  
AKHAVAN MS, 1976, P NATL ACAD SCI USA, V73, P882
[2]   GLOBIN CHAIN ELECTROPHORESIS - A NEW APPROACH TO THE DETERMINATION OF THE G-GAMMA/A-GAMMA RATIO IN FETAL HEMOGLOBIN AND TO STUDIES OF GLOBIN-SYNTHESIS [J].
ALTER, BP ;
GOFF, SC ;
EFREMOV, GD ;
GRAVELY, ME ;
HUISMAN, THJ .
BRITISH JOURNAL OF HAEMATOLOGY, 1980, 44 (04) :527-534
[3]  
BARWICK R C, 1981, Texas Reports on Biology and Medicine, V40, P143
[4]  
BASSET P, 1978, BLOOD, V51, P971
[5]   ESTIMATION OF SMALL PERCENTAGES OF FOETAL HAEMOGLOBIN [J].
BETKE, K ;
MARTI, HR ;
SCHLICHT, I .
NATURE, 1959, 184 (4702) :1877-1878
[6]   STRUCTURAL STUDY OF HEMOGLOBIN HAZEBROUCK, BETA-38(C4)TH-]PRO - A NEW ABNORMAL HEMOGLOBIN WITH INSTABILITY AND LOW OXYGEN-AFFINITY [J].
BLOUQUIT, Y ;
DELANOEGARIN, J ;
LACOMBE, C ;
AROUS, N ;
CAYRE, Y ;
PEDUZZI, J ;
BRACONNIER, F ;
GALACTEROS, F .
FEBS LETTERS, 1984, 172 (02) :155-158
[7]  
BRACONNIER F, 1975, NOUV REV FR HEMATOL, V15, P527
[8]  
BUNN HF, 1979, COMP BIOCHEM PHYS A, V62, P95
[9]   HEMOGLOBIN CRANSTON, AN UNSTABLE VARIANT HAVING AN ELONGATED BETA-CHAIN DUE TO NONHOMOLOGOUS CROSSOVER BETWEEN 2 NORMAL BETA-CHAIN GENES [J].
BUNN, HF ;
SCHMIDT, GJ ;
HANEY, DN ;
DLUHY, RG .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (09) :3609-3613
[10]   SIMPLE METHOD FOR DETECTION OF UNSTABLE HEMOGLOBINS [J].
CARRELL, RW ;
KAY, R .
BRITISH JOURNAL OF HAEMATOLOGY, 1972, 23 (05) :615-&