HYALINOSIS-CUTIS-ET-MUCOSAE - REVIEW WITH A CASE-REPORT

被引:13
作者
CHAUDHARY, SJ [1 ]
DAYAL, PK [1 ]
机构
[1] GOVT DENT COLL & HOSP,DEPT ORAL MED & RADIOL,NAGPUR,MAHARASHTRA,INDIA
来源
ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTICS | 1995年 / 80卷 / 02期
关键词
D O I
10.1016/S1079-2104(05)80196-9
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Hyalinosis cutis et mucosae (lipoid proteinosis) is a rare disorder characterized by hyaline and lipid deposits in the skin and mucous membrane of the oral cavity, upper respiratory tract, and internal organs. It usually appears in infancy with hoarseness. This disorder is particularly interesting because of its rarity and wide range of clinical manifestations. We report a case that demonstrated manifestations of lipoid proteinosis.
引用
收藏
页码:168 / 171
页数:4
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