INCREASED BREAKDOWN OF GLYCOSAMINOGLYCANS AND APPEARANCE OF CORRECTIVE ENZYME AFTER SKIN TRANSPLANTS IN HUNTER SYNDROME

被引：34

作者：

DEAN, MF

MUIR, H

BENSON, PF

BUTTON, LR

BATCHELOR, JR

BEWICK, M

机构：

[1] KENNEDY INST RHEUMATOL,BIOCHEM DIV,BUTE GARDENS,LONDON W6 7DW,ENGLAND

[2] GUYS HOSP,MED SCH,DEPT SURG,PAEDIAT RES UNIT,LONDON SE1 9RT,ENGLAND

来源：

关键词：

D O I：

10.1038/257609a0

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：609 / 612

页数：4

共 16 条

[1] DEFECT IN HUNTER SYNDROME - DEFICIENCY OF SULFOIDURONATE SULFATASE
BACH, G
EISENBERG, F
CANTZ, M
NEUFELD, EF
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1973, 70 (07) : 2134 - 2138
[2] BITTER T, 1962, ANAL BIOCHEM, V4, P303
[3] CANTZ M, 1972, J BIOL CHEM, V247, P5456
[4] DANES, 1972, LANCET, V2, P883
[5] MOBILIZATION OF GLYCOSAMINOGLYCANS BY PLASMA INFUSION IN MUCOPOLY-SACCHARIDOSIS TYPE-III - 2 TYPES OF RESPONSE
DEAN, MF
MUIR, H
BENSON, PF
[J]. NATURE-NEW BIOLOGY, 1973, 243 (126): : 143 - 146
[6] HURLERS, HUNTERS AND MORQUIOS SYNDROMES - BIOCHEMICAL STUDY IN LIGHT OF CURRENT VIEWS OF UNDERLYING DEFECTS
DEAN, MF
MUIR, H
EWINS, RJF
[J]. BIOCHEMICAL JOURNAL, 1971, 123 (05) : 883 - &
[7] DEAN MF, 1973, 3RD P INT C INT ASS
[8] DEAN MF, 1973, TREATMENT INBORN ERR, P227
[9] DEAN MF, 1974, PEDIATRIC RES, V8, P2
[10] DEKABAN AS, 1972, PEDIATRICS, V50, P688