A NEW AMINO-ACID MIXTURE PERMITS NEW APPROACHES TO THE TREATMENT OF PHENYLKETONURIA

被引：12

作者：

BUIST, NRM

PRINCE, AP

HUNTINGTON, KL

TUERCK, JM

WAGGONER, DD

机构：

[1] OREGON HLTH SCI UNIV,DEPT MOLEC & MED GENET,PORTLAND,OR 97207

[2] OREGON HLTH SCI UNIV,DEPT NUTR,PORTLAND,OR 97207

[3] OREGON HLTH SCI UNIV,DEPT CRIPPLED CHILDRENS DIV,PORTLAND,OR 97207

[4] OREGON HLTH SCI UNIV,DEPT NEUROL,PORTLAND,OR 97207

来源：

ACTA PAEDIATRICA | 1994年 / 83卷

关键词：

AMINO ACIDS; DIETARY COMPLIANCE; ELEMENTAL MEDICAL FOODS; PHENYLKETONURIA;

D O I：

10.1111/j.1651-2227.1994.tb13458.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

A new amino acid mixture for incorporation into medical foods for the treatment of hyperphenylalaninemia has been tested in a regular clinic. The mix is designed to be as unobtrusive as possible, consistent with good nutrition. After more than 1 year of trial as a beverage, we have shown that it is safe and well tolerated but that plasma phenylalanine is no better controlled than with some other products. The mix can be incorporated into a large number of different foods without affecting the taste. Occult monitoring of the quantity of medical foods purchased compared with the amounts reported to be consumed in diet histories provides an excellent way to monitor dietary compliance.

引用

页码：75 / 77

页数：3