CONTINUOUS VENOVENOUS HEMOFILTRATION IN THE MANAGEMENT OF ACUTE DECOMPENSATION IN INBORN-ERRORS OF METABOLISM

被引：55

作者：

THOMPSON, GN

BUTT, WW

SHANN, FA

KIRBY, DM

HENNING, RD

HOWELLS, DW

OSBORNE, A

机构：

[1] ROYAL CHILDRENS HOSP, INTENS CARE UNIT, PARKVILLE, VIC 3052, AUSTRALIA

[2] UNIV MELBOURNE, MURDOCH INST, DEPT PAEDIAT, PARKVILLE, VIC 3052, AUSTRALIA

来源：

JOURNAL OF PEDIATRICS | 1991年 / 118卷 / 06期

关键词：

D O I：

10.1016/S0022-3476(05)82198-5

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Continuous venovenous hemofiltration was used to treat two neonates, one with maple syrup urine disease and the other with an inborn error of long-chain fatty acid oxidation. The latter infant had hypoglycemia, hyperammonemia and lactic acidosis. In both cases, acceptable biochemical control was achieved within 8 hours. This therapy offers the potential to overcome acute crises rapidly in a wide range of inborn errors of intermediary metabolism.

引用

页码：879 / 884

页数：6

共 10 条

[1]

Goodman S I, 1986, Adv Pediatr, V33, P197

[2]

KRAMER P, 1980, INT J ARTIF ORGANS, V3, P225

[3] CONTINUOUS ARTERIOVENOUS HEMOFILTRATION IN THE CRITICALLY ILL PATIENT - CLINICAL USE AND OPERATIONAL CHARACTERISTICS [J].