LYMPHANGIOMYOMATOSIS RECURRENCE IN THE ALLOGRAFT AFTER SINGLE-LUNG TRANSPLANTATION

被引:65
作者
OBRIEN, JD
LIUM, JH
PAROSA, JF
DEYOUNG, BR
WICK, MR
TRULOCK, EP
机构
[1] WASHINGTON UNIV,SCH MED,DEPT MED,DIV PULM & CRIT CARE MED,ST LOUIS,MO 63110
[2] WASHINGTON UNIV,SCH MED,DEPT SURG,ST LOUIS,MO 63110
[3] WASHINGTON UNIV,SCH MED,DEPT PATHOL,ST LOUIS,MO 63110
[4] WASHINGTON UNIV,SCH MED,LUNG TRANSPLANT PROGRAM,ST LOUIS,MO 63110
[5] BARNES HOSP,ST LOUIS,MO 63110
[6] SALEM HOSP,DEPT MED,SALEM,OR
[7] SALEM HOSP,DEPT PATHOL,SALEM,OR
关键词
D O I
10.1164/ajrccm.151.6.7767554
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
The evolution of lung transplantation has offered an additional treatment option for patients with a variety of end-stage lung diseases, including some with systemic disorders. Lymphangiomyomatosis (LAM) is a multisystem disease of premenopausal women. The lung is the most frequently involved vital organ, and respiratory failure is the most common case of death. A small number of patients with LAM have undergone lung transplantation. This report describes a case of recurrent LAM in the allograft after single lung transplantation and discusses the implications of this finding.
引用
收藏
页码:2033 / 2036
页数:4
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