FETAL RHABDOMYOMA AND NEVOID BASAL-CELL CARCINOMA SYNDROME

被引:25
作者
DISANTO, S
ABT, AB
BOAL, DK
KRUMMEL, TM
机构
[1] PENN STATE UNIV,MILTON S HERSHEY MED CTR,DEPT PATHOL,POB 850,HERSHEY,PA 17033
[2] PENN STATE UNIV,MILTON S HERSHEY MED CTR,DEPT RADIOL,HERSHEY,PA 17033
[3] PENN STATE UNIV,MILTON S HERSHEY MED CTR,DEPT SURG,HERSHEY,PA 17033
来源
PEDIATRIC PATHOLOGY | 1992年 / 12卷 / 03期
关键词
FETAL RHABDOMYOMA; NEVOID BASAL CELL CARCINOMA;
D O I
10.3109/15513819209023323
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
A 6-year-old white female presented with a fetal rhabdomyoma of the posterior mediastinum and retroperitoneum. Radiologic evaluation and family history revealed features of the nevoid basal cell carcinoma syndrome (NBS). Literature review disclosed two other children with NBS and fetal rhabdomyoma, which should be regarded as one of the soft tissue tumors associated with NBS.
引用
收藏
页码:441 / 447
页数:7
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