METABOLIC STUDIES IN TYROSINEMIA

被引:2
作者
BUIST, NRM
FELLMAN, JH
KENNAWAY, N
机构
关键词
D O I
10.1203/00006450-197801000-00014
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
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页码:56 / 57
页数:2
相关论文
共 12 条
[1]  
BORUD O, 1971, ACTA PHARMACOL TOX, V30, P185
[2]  
BUIST NRM, 1974, HERITABLE DISORDERS, P160
[3]   METABOLIC STUDIES ON 2 PATIENTS WITH NON-HEPATIC TYROSINEMIA USING DEUTERATED TYROSINE LOADS [J].
FAULL, KF ;
GAN, I ;
HALPERN, B ;
HAMMOND, J ;
IM, S ;
COTTON, RGH ;
DANKS, DM .
PEDIATRIC RESEARCH, 1977, 11 (05) :631-637
[4]   ASSAY, PROPERTIES AND TISSUE DISTRIBUTION OF PARA HYDROXYPHENYLPYRUVATE HYDROXYLASE [J].
FELLMAN, JH ;
ROTH, ES ;
FUJITA, TS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 284 (01) :90-&
[5]   SOURCE OF AROMATIC KETOACIDS IN TYROSINEMIA AND PHENYLKETONURIA [J].
FELLMAN, JH ;
SWANSON, RE ;
BUIST, NRM ;
KENNAWAY, NG .
CLINICA CHIMICA ACTA, 1972, 39 (01) :243-&
[6]   SOLUBLE AND MITOCHONDRIAL FORMS OF TYROSINE AMINOTRANSFERASE . RELATIONSHIP TO HUMAN TYROSINEMIA [J].
FELLMAN, JH ;
VANBELLI.PJ ;
JONES, RT ;
KOLER, RD .
BIOCHEMISTRY, 1969, 8 (02) :615-+
[7]   DECARBOXYLATION TO TYRAMINE IS NOT A MAJOR ROUTE OF TYROSINE METABOLISM IN MAMMALS [J].
FELLMAN, JH ;
ROTH, ES ;
FUJITA, TS .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1976, 174 (02) :562-567
[8]   METABOLIC STUDIES IN A PATIENT WITH HEPATIC CYTOSOL TYROSINE AMINOTRANSFERASE DEFICIENCY [J].
KENNAWAY, NG ;
BUIST, NRM .
PEDIATRIC RESEARCH, 1971, 5 (07) :287-&
[9]   ORIGIN OF URINARY PARA HYDROXYPHENYLPYRUVATE IN A PATIENT WITH HEPATIC CYTOSOL TYROSINE AMINOTRANSFERASE DEFICIENCY [J].
KENNAWAY, NG ;
BUIST, NRM ;
FELLMAN, JH .
CLINICA CHIMICA ACTA, 1972, 41 (01) :157-&