MOLECULAR PATHOLOGY OF FABRYS-DISEASE - PHYSICAL AND KINETIC-PROPERTIES OF ALPHA-GALACTOSIDASE A IN CULTURED HUMAN ENDOTHELIAL CELLS

被引：12

作者：

JOHNSON, DL

DESNICK, RJ

机构：

[1] UNIV MINNESOTA,DEPT PEDIAT,MINNEAPOLIS,MN 55455

[2] UNIV MINNESOTA,DWIGHT INST HUMAN GENET,MINNEAPOLIS,MN 55455

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1978年 / 538卷 / 02期

关键词：

D O I：

10.1016/0304-4165(78)90346-X

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：195 / 204

页数：10

共 31 条

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[9]

DESNICK RJ, 1973, J PEDIATR-US, V83, P149

[10]

DESNICK RJ, 1973, J LAB CLIN MED, V81, P157

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