INCREASED COPPER METALLOTHIONEIN IN MENKES CULTURED SKIN FIBROBLASTS

被引:46
作者
LABADIE, GU [1 ]
HIRSCHHORN, K [1 ]
KATZ, S [1 ]
BERATIS, NG [1 ]
机构
[1] NEW YORK STATE INST BASIC RES MENTAL RETARDAT,DEPT HUMAN GENET,STATEN ISL,NY 10314
关键词
D O I
10.1203/00006450-198103000-00012
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:257 / 261
页数:5
相关论文
共 19 条
[1]   CU-64 METABOLISM IN MENKES AND NORMAL CULTURED SKIN FIBROBLASTS [J].
BERATIS, NG ;
PRICE, P ;
LABADIE, G ;
HIRSCHHORN, K .
PEDIATRIC RESEARCH, 1978, 12 (06) :699-702
[2]   EFFECT OF COPPER ON MENKES AND NORMAL CULTURED SKIN FIBROBLASTS [J].
BERATIS, NG ;
YEE, M ;
LABADIE, GU ;
HIRSCHHORN, K .
DEVELOPMENTAL PHARMACOLOGY AND THERAPEUTICS, 1980, 1 (05) :305-317
[3]   ISOLATION OF (COPPER, ZINC)-THIONEINS FROM LIVERS OF COPPER INJECTED RATS [J].
BREMNER, I ;
YOUNG, BW .
BIOCHEMICAL JOURNAL, 1976, 157 (02) :517-520
[4]  
BREMNER I, 1974, BIOCHEM SOC T, V2, P425
[5]   CELL-CULTURE STUDIES OF MENKES KINKY HAIR DISEASE [J].
CHAN, WY ;
GARNICA, AD ;
RENNERT, OM .
CLINICA CHIMICA ACTA, 1978, 88 (03) :495-507
[6]   INDUCIBILITY OF METALLOTHIONEIN BIOSYNTHESIS IN CULTURED NORMAL AND MENKES KINKY HAIR DISEASE FIBROBLASTS - EFFECTS OF COPPER AND CADMIUM [J].
CHAN, WY ;
GARNICA, AD ;
RENNERT, OM .
PEDIATRIC RESEARCH, 1979, 13 (03) :197-203
[7]  
DANKS DM, 1972, LANCET, V1, P1100
[8]  
DANKS DM, 1972, PEDIATRICS, V50, P188
[9]   MENKES KINKY HAIR DISEASE - FURTHER DEFINITION OF DEFECT IN COPPER TRANSPORT [J].
DANKS, DM ;
CARTWRIGHT, E ;
STEVENS, BJ ;
TOWNLEY, RRW .
SCIENCE, 1973, 179 (4078) :1140-1142