CHRONIC INTRAHEPATIC CHOLESTASIS IN SICKLE-CELL DISEASE REQUIRING EXCHANGE-TRANSFUSION

被引:33
作者
OCALLAGHAN, A
OBRIEN, SG
NINKOVIC, M
BUTCHER, GP
FOSTER, CS
WALTERS, JRF
ROBERTS, IAG
机构
[1] ROYAL POSTGRAD MED SCH,DEPT HAEMATOL,LONDON W12 0HS,ENGLAND
[2] ROYAL POSTGRAD MED SCH,DEPT GASTROENTEROL,LONDON,ENGLAND
[3] UNIV LIVERPOOL,DEPT PATHOL,LIVERPOOL L69 3BX,MERSEYSIDE,ENGLAND
关键词
SICKLE CELL DISEASE; INTRAHEPATIC CHOLESTASIS; HYPERBILIRUBINEMIA;
D O I
10.1136/gut.37.1.144
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
A 15 year old boy with sickle cell disease developed intrahepatic cholestasis. A course of exchange transfusion successfully corrected the extreme hyperbilirubinaemia over one year. Upon stopping the exchange transfusion programme the hyperbilirubinaemia relapsed but transfusion was effective when reinstituted.
引用
收藏
页码:144 / 147
页数:4
相关论文
共 12 条
[1]
BENIGN COURSE OF EXTREME HYPERBILIRUBINEMIA IN SICKLE-CELL ANEMIA - ANALYSIS OF 6 CASES [J].
BUCHANAN, GR ;
GLADER, BE .
JOURNAL OF PEDIATRICS, 1977, 91 (01) :21-24
[2]
COMER GM, 1991, AM J GASTROENTEROL, V86, P1232
[3]
GREEN TW, 1953, B JOHNS HOPKINS HOSP, V92, P99
[4]
HARGROVE MD, 1970, DIGEST DIS, V15, P437
[5]
LIVER INVOLVEMENT IN SICKLE-CELL DISEASE [J].
JOHNSON, CS ;
OMATA, M ;
TONG, MJ ;
SIMMONS, JF ;
WEINER, J ;
TATTER, D .
MEDICINE, 1985, 64 (05) :349-356
[6]
LUTHER R, 1988, ARCH PATHOL LAB MED, V112, P290
[7]
PATHOLOGICAL SPECTRUM OF LIVER-DISEASES IN SICKLE-CELL DISEASE [J].
OMATA, M ;
JOHNSON, CS ;
TONG, M ;
TATTER, D .
DIGESTIVE DISEASES AND SCIENCES, 1986, 31 (03) :247-256
[8]
AN UNUSUAL HEPATIC SEQUELA OF SICKLE CELL ANEMIA - A REPORT OF 5 CASES [J].
OWEN, DM ;
ALDRIDGE, JE ;
THOMPSON, RB .
AMERICAN JOURNAL OF THE MEDICAL SCIENCES, 1965, 249 (02) :175-&
[9]
ROSENBLATE HJ, 1970, ARCH PATHOL, V90, P235
[10]
EXCHANGE-TRANSFUSION FOR SICKLE-CELL INTRA-HEPATIC CHOLESTASIS [J].
SHEEHY, TW ;
LAW, DE ;
WADE, BH .
ARCHIVES OF INTERNAL MEDICINE, 1980, 140 (10) :1364-1366