PRIMARY MIDLINE DEVELOPMENTAL FIELD .2. CLINICAL EPIDEMIOLOGIC ANALYSIS OF ALTERATION OF LATERALITY (NORMAL BODY SYMMETRY AND ASYMMETRY)

被引:24
作者
MARTINEZFRIAS, ML
URIOSTE, M
BERMEJO, E
RODRIGUEZPINILLA, E
FELIX, V
PAISAN, L
MARTINEZ, S
EGUES, J
GOMEZ, F
APARICIO, P
CUCALON, F
ARROYO, A
MEIPP, C
VAZQUEZ, S
RODRIGUEZ, JI
ROSA, A
GARCIA, J
JIMENEZ, N
MORO, C
机构
[1] UNIV COMPLUTENSE MADRID, HOSP SAN CARLOS, E-28040 MADRID, SPAIN
[2] HOSP LA PAZ, SERV ANAT PATOL, MADRID, SPAIN
[3] HOSP DR TRUETA, SERV PEDIAT, GIRONA, SPAIN
[4] HOSP VIRGEN CAMINO, SERV NEONATOL, PAMPLONA, SPAIN
[5] HOSP VIRGEN MONTE TORO, SERV PEDIAT, MENORCA, SPAIN
[6] HOSP GEN YAGUE, SERV PEDIAT, BURGOS, SPAIN
[7] COMPLEJO HOSP SAN MILLAN, SERV PEDIAT, LOGRONO, SPAIN
[8] HOSP VIRGEN CONCHA, SERV TOCOGINECOL, ZAMORA, SPAIN
[9] HOSP GEN ALICANTE, SERV PEDIAT, ALACANT, SPAIN
[10] CTR ESPECIALIDADES ELX, ALACANT, SPAIN
[11] HOSP GEN ALBACETE, SERV NEONATOL, ALBACETE, SPAIN
[12] HOSP NUESTRA SENORA ALARCOS, SERV PEDIAT, CIUDAD REAL, SPAIN
[13] HOSP MONTECELO, SERV PEDIAT, PONTEVEDRA, SPAIN
[14] HOSP GEN SEGOVIA, SERV OBSTET & GINECOL, SEGOVIA, SPAIN
[15] HOSP VIRGEN SALUD, SERV PEDIAT, TOLEDO, SPAIN
[16] HOSP GEN ASTURIAS, SERV PEDIAT, E-33006 OVIEDO, SPAIN
[17] HOSP N S ARANZAZU, SERV PEDIAT, SAN SEBASTIAN, SPAIN
来源
AMERICAN JOURNAL OF MEDICAL GENETICS | 1995年 / 56卷 / 04期
关键词
MIDLINE; DEVELOPMENTAL FIELD DEFECTS; EPIDEMIOLOGY; SYMMETRY; ASYMMETRY; LATERALITY SEQUENCES; ASPLENIA; POLYSPLENIA;
D O I
10.1002/ajmg.1320560407
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
Lubinsky [Am J Med Genet 3:23-28, 1987] has suggested that the properties of the midline involve early determinative informational processes and are related to the midline's position and definition of the body's plane of symmetry. Opitz [Am J Med Genet 21:175-176, 1985, BD: OAS XXIX(1):3-37 1993] has pointed out that the laterality sequences represent a midline developmental held complex, Thus, bilateral left-sidedness (with asplenia) and bilateral right-sidedness (with polysplenia) have been considered laterality sequences or syndromes if cause is known, Using the malformed infants registered by the Spanish Collaborative Study of Congenital Malformations (ECEMC), we performed a clinical/epidemiological analysis of the relationship between midline defects and alteration of normal body asymmetry and symmetry. The results support the assumption that both conditions could be consequence of disturbances in the midline primary developmental field. (C) 1995 Wiley-Liss, Inc.
引用
收藏
页码:382 / 388
页数:7
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