BIOSYNTHESIS OF TETRAHYDROBIOPTERIN - A SENSITIVE ASSAY OF 6-PYRUVOYLTETRAHYDROPTERIN SYNTHASE USING [2'-H-3]DIHYDRONEOPTERIN 3'-TRIPHOSPHATE AS SUBSTRATE

被引:18
作者
KERLER, F
SCHWARZKOPF, B
KATZENMAIER, G
LEVAN, Q
SCHMID, C
ZIEGLER, I
BACHER, A
机构
[1] TECH UNIV MUNICH, LEHRSTUHL ORGAN CHEM & BIOCHEM, LICHTENBERGSTR 4, D-8046 GARCHING, GERMANY
[2] GESELL STRAHLEN & UMWELTFORSCH MBH, INST EXPTL HAMATOL, MUNICH, GERMANY
关键词
D O I
10.1016/S0304-4165(89)80005-4
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:15 / 17
页数:3
相关论文
共 14 条
[1]   TETRAHYDROBIOPTERIN BIOSYNTHESIS - STUDIES WITH SPECIFICALLY LABELED (H-2)NAD(P)H AND (H2O)-H-2 AND OF THE ENZYMES INVOLVED [J].
CURTIUS, HC ;
HEINTEL, D ;
GHISLA, S ;
KUSTER, T ;
LEIMBACHER, W ;
NIEDERWIESER, A .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 148 (03) :413-419
[2]   ANALYSIS OF REDUCED FORMS OF BIOPTERIN IN BIOLOGICAL TISSUES AND FLUIDS [J].
FUKUSHIMA, T ;
NIXON, JC .
ANALYTICAL BIOCHEMISTRY, 1980, 102 (01) :176-188
[3]  
HASLER T, 1986, P319
[4]   PURIFICATION AND PROPERTIES OF THE PHOSPHATE ELIMINATING ENZYME INVOLVED IN THE BIOSYNTHESIS OF BH4 IN MAN [J].
HEINTEL, D ;
LEIMBACHER, W ;
REDWEIK, U ;
ZAGALAK, B ;
CURTIUS, HC .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1985, 127 (01) :213-219
[5]  
MILSTIEN S, 1986, P169
[6]   BIOSYNTHESIS AND METABOLISM OF TETRAHYDROBIOPTERIN AND MOLYBDOPTERIN [J].
NICHOL, CA ;
SMITH, GK ;
DUCH, DS .
ANNUAL REVIEW OF BIOCHEMISTRY, 1985, 54 :729-764
[7]   TETRAHYDROBIOPTERIN DEFICIENCY - ASSAY FOR 6-PYRUVOYL-TETRAHYDROPTERIN SYNTHASE ACTIVITY IN ERYTHROCYTES, AND DETECTION OF PATIENTS AND HETEROZYGOUS CARRIERS [J].
SHINTAKU, H ;
NIEDERWIESER, A ;
LEIMBACHER, W ;
CURTIUS, HC .
EUROPEAN JOURNAL OF PEDIATRICS, 1988, 147 (01) :15-19
[8]   2 NEW TETRAHYDROPTERIN INTERMEDIATES IN THE ADRENAL-MEDULLARY DENOVO BIOSYNTHESIS OF TETRAHYDROBIOPTERIN [J].
SMITH, GK ;
NICHOL, CA .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1984, 120 (03) :761-766
[9]  
SMITH GK, 1986, J BIOL CHEM, V261, P2725
[10]  
SWITCHENKO AC, 1985, J BIOL CHEM, V260, P2945