COMPLETE AND PARTIAL DEFICIENCIES OF COMPLEMENT FACTOR-D IN A DUTCH FAMILY

被引:65
作者
HIEMSTRA, PS
LANGELER, E
COMPIER, B
KEEPERS, Y
LEIJH, PCJ
VANDENBARSELAAR, MT
OVERBOSCH, D
DAHA, MR
机构
[1] UNIV HOSP LEIDEN,DEPT NEPHROL,2300 RC LEIDEN,NETHERLANDS
[2] RED CROSS HOSP,THE HAGUE,NETHERLANDS
关键词
D O I
10.1172/JCI114384
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1957 / 1961
页数:5
相关论文
共 29 条
[1]   INCREASED SUSCEPTIBILITY TO INFECTION ASSOCIATED WITH ABNORMALITIES OF COMPLEMENT-MEDIATED FUNCTIONS AND OF THIRD COMPONENT OF COMPLEMENT (C3) [J].
ALPER, CA ;
ABRAMSON, N ;
JOHNSTON, RB ;
JANDL, JH ;
ROSEN, FS .
NEW ENGLAND JOURNAL OF MEDICINE, 1970, 282 (07) :349-&
[2]   QUANTITATION OF COMPLEMENT FACTOR-D IN HUMAN-SERUM BY A SOLID-PHASE RADIOIMMUNOASSAY [J].
BARNUM, SR ;
NIEMANN, MA ;
KEARNEY, JF ;
VOLANAKIS, JE .
JOURNAL OF IMMUNOLOGICAL METHODS, 1984, 67 (02) :303-309
[3]  
DAHA MR, 1982, CLIN EXP IMMUNOL, V48, P733
[4]  
DAHA MR, 1981, IMMUNOLOGY, V43, P513
[5]  
ENG RHK, 1978, CLIN RES, V26, pA394
[6]   PROPERDIN FACTOR D - CHARACTERIZATION OF ITS ACTIVE-SITE AND ISOLATION OF PRECURSOR FORM [J].
FEARON, DT ;
AUSTEN, KF ;
RUDDY, S .
JOURNAL OF EXPERIMENTAL MEDICINE, 1974, 139 (02) :355-366
[7]   INHERITED DEFICIENCIES OF COMPLEMENT AND COMPLEMENT-RELATED PROTEINS [J].
FRIES, LF ;
OSHEA, JJ ;
FRANK, MM .
CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1986, 40 (01) :37-49
[8]   INHERITED DEFICIENCY OF 2ND COMPONENT OF COMPLEMENT - RHEUMATIC DISEASE ASSOCIATIONS [J].
GLASS, D ;
RAUM, D ;
GIBSON, D ;
STILLMAN, JS ;
SCHUR, PH .
JOURNAL OF CLINICAL INVESTIGATION, 1976, 58 (04) :853-861
[9]  
JOHNSON U, 1983, ACTA PATHOL MICROB C, V91, P1447
[10]  
KLUINNELEMANS HC, 1984, CLIN EXP IMMUNOL, V58, P724