ATP DEPLETION AS A CONSEQUENCE OF ADENOSINE-DEAMINASE INHIBITION IN MAN

被引:128
作者
SIAW, MFE
MITCHELL, BS
KOLLER, CA
COLEMAN, MS
HUTTON, JJ
机构
[1] UNIV MICHIGAN, SIMPSON MEM INST, DEPT INTERNAL MED, ANN ARBOR, MI 48109 USA
[2] UNIV KENTUCKY, DEPT MED, LEXINGTON, KY 40536 USA
[3] VET ADM HOSP, LEXINGTON, KY 40536 USA
来源
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1980年 / 77卷 / 10期
关键词
D O I
10.1073/pnas.77.10.6157
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:6157 / 6161
页数:5
相关论文
共 34 条
[1]  
BOLLUM FJ, 1966, PROCEDURES NUCLEIC A, P296
[2]  
CARSON DA, 1978, J IMMUNOL, V121, P1726
[3]   LYMPHO-SPECIFIC TOXICITY IN ADENOSINE-DEAMINASE DEFICIENCY AND PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY - POSSIBLE ROLE OF NUCLEOSIDE KINASE(S) [J].
CARSON, DA ;
KAYE, J ;
SEEGMILLER, JE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (12) :5677-5681
[5]   ADENOSINE-DEAMINASE DEFICIENCY - DISAPPEARANCE OF ADENINE DEOXYNUCLEOTIDES FROM A PATIENTS ERYTHROCYTES AFTER SUCCESSFUL MARROW TRANSPLANTATION [J].
CHEN, SH ;
OCHS, HD ;
SCOTT, CR ;
GIBLETT, ER ;
TINGLE, AJ .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (06) :1386-1389
[6]   DEOXYADENOSINE TRIPHOSPHATE AS A POTENTIALLY TOXIC METABOLITE IN ADENOSINE-DEAMINASE DEFICIENCY [J].
COHEN, A ;
HIRSCHHORN, R ;
HOROWITZ, SD ;
RUBINSTEIN, A ;
POLMAR, SH ;
HONG, R ;
MARTIN, DW .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1978, 75 (01) :472-476
[7]  
COLEMAN MS, 1978, J BIOL CHEM, V253, P1619
[8]   OVERPRODUCTION OF ADENINE DEOXYNUCLEOSIDES AND DEOXYNUCLEOTIDES IN ADENOSINE-DEAMINASE DEFICIENCY WITH SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].
DONOFRIO, J ;
COLEMAN, MS ;
HUTTON, JJ ;
DAOUD, A ;
LAMPKIN, B ;
DYMINSKI, J .
JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (04) :884-887
[9]   ROLE OF ADENOSINE AND 2'-DEOXYADENOSINE IN MAMMALIAN-CELLS [J].
FOX, IH ;
KELLEY, WN .
ANNUAL REVIEW OF BIOCHEMISTRY, 1978, 47 :655-686
[10]  
GIBLETT ER, 1972, LANCET, V2, P1067