BETA-GALACTOSIDASE, N-ACETYL-BETA-GLUCOSAMINIDASE, AND BETA-GLUCURONIDASE ACTIVITY IN FIBROBLAST CULTURES FROM PATIENTS WITH MUCOPOLYSACCHARIDE STORAGE-DISEASE

被引：7

作者：

LAGUNOFF, D

PRITZL, P

SCOTT, CR

机构：

[1] UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195

[2] UNIV WASHINGTON,DEPT PATHOL,SEATTLE,WA 98195

来源：

BIOCHEMICAL MEDICINE | 1973年 / 7卷 / 03期

关键词：

D O I：

10.1016/0006-2944(73)90055-0

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：343 / 349

页数：7

共 18 条

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[2] BENSON PF, 1970, NEW ENGL J MED, V283, P999
[3] ACID GLYCOSIDASES IN MUCOPOLYSACCHARIDOSES FIBROBLASTS
FLUHARTY, AL
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KIHARA, H
[J]. BIOCHEMICAL MEDICINE, 1970, 4 (02): : 110 - &
[4] DEFECT IN HURLERS AND HUNTERS SYNDROMES - FAULTY DEGRADATION OF MUCOPOLYSACCHARIDE
FRATANTONI, JC
HALL, CW
NEUFELD, EF
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1968, 60 (02) : 699 - +
[5] KRESSE H, 1972, J BIOL CHEM, V247, P2164
[6] LAGUNOFF D, 1967, P SOC EXP BIOL MED, V126, P34
[7] LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8] BETA-GALACTOSIDASE DEFICIENCY IN HURLER SYNDROME
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OKADA, S
WOOLLACOTT
PATEL, V
HO, MW
TAPPEL, AL
OBRIEN, JS
[J]. NEW ENGLAND JOURNAL OF MEDICINE, 1969, 281 (07) : 338 - &
[9] HURLERS SYNDROME, AN ALPHA-L-IDURONIDASE DEFICIENCY
MATALON, R
DORFMAN, A
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 47 (04) : 959 - &
[10] L-IDURONIDASE IN CULTURED HUMAN FIBROBLASTS AND LIVER
MATALON, R
CIFONELLI, JA
DORFMAN, A
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1971, 42 (02) : 340 - +