CORONARY-ARTERY ANEURYSM WITHOUT STENOSIS IN ASSOCIATION WITH OSLER-WEBER-RENDU DISEASE - A CASE-REPORT

A fifty-three-year-old woman presented with coronary artery aneurysm in association with Osler-Weber-Rendu disease (hereditary hemorrhagic telangiectasia) manifested also by large pulmonary arteriovenous fistulas. The arterial dye dilution curves were unusually distorted owing to the right-to-left shunts. The coronary artery aneurysm was located in multiple sites but was not accompanied by stenotic lesions. Coronary artery aneurysm without stenosis is is a rare pathologic state and has not been previously reported in associated with hereditary telangiectasia.