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ISOELECTRIC-FOCUSING OF ACID-HYDROLASES IN HUMAN LIVER AND SERUM - FINDINGS IN SERA FROM ONE PATIENT WITH I-CELL DISEASE PHENOTYPE
被引:8
作者
:
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
HULTBERG, B
机构
:
来源
:
CLINICA CHIMICA ACTA
|
1978年
/ 88卷
/ 03期
关键词
:
D O I
:
10.1016/0009-8981(78)90279-6
中图分类号
:
R446 [实验室诊断];
R-33 [实验医学、医学实验];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:441 / 448
页数:8
相关论文
共 19 条
[1]
ASHWELL G, 1974, ADV ENZYMOL RAMB, V41, P99
[2]
CHESTER MA, 1977, THESIS LUND, P91
[3]
DENTANDT WR, 1974, J LAB CLIN MED, V83, P403
[4]
TISSUE FRACTIONATION STUDIES .6. INTRACELLULAR DISTRIBUTION PATTERNS OF ENZYMES IN RAT-LIVER TISSUE
DUVE, CD
论文数:
0
引用数:
0
h-index:
0
DUVE, CD
PRESSMAN, BC
论文数:
0
引用数:
0
h-index:
0
PRESSMAN, BC
GIANETTO, R
论文数:
0
引用数:
0
h-index:
0
GIANETTO, R
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
APPELMANS, F
论文数:
0
引用数:
0
h-index:
0
APPELMANS, F
[J].
BIOCHEMICAL JOURNAL,
1955,
60
(1-4)
: 604
-
617
[5]
PHYSICOCHEMICAL MODIFICATIONS OF LYSOSOMAL HYDROLASES DURING INTRACELLULAR TRANSPORT
GOLDSTONE, A
论文数:
0
引用数:
0
h-index:
0
机构:
VET ADM RES HOSP, NEUROL SERV, CHICAGO, IL 60611 USA
GOLDSTONE, A
KOENIG, H
论文数:
0
引用数:
0
h-index:
0
机构:
VET ADM RES HOSP, NEUROL SERV, CHICAGO, IL 60611 USA
KOENIG, H
[J].
BIOCHEMICAL JOURNAL,
1973,
132
(02)
: 267
-
+
[6]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
: 992
-
&
[7]
ROLE OF GLYCOSIDICALLY BOUND MANNOSE IN ASSIMILATION OF BETA-GALACTOSIDASE BY GENERALIZED GANGLIOSIDOSIS FIBROBLASTS
HIEBER, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
HIEBER, V
DISTLER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
DISTLER, J
MYEROWITZ, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
MYEROWITZ, R
SCHMICKEL, RD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
SCHMICKEL, RD
JOURDIAN, GW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
JOURDIAN, GW
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1976,
73
(03)
: 710
-
717
[8]
ARTIFICIAL SUBSTRATES IN ASSAY OF ACID GLYCOSIDASES
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
HULTBERG, B
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
OCKERMAN, PA
[J].
CLINICA CHIMICA ACTA,
1972,
39
(01)
: 49
-
&
[9]
PHOSPHOHEXOSYL COMPONENTS OF A LYSOSOMAL ENZYME ARE RECOGNIZED BY PINOCYTOSIS RECEPTORS ON HUMAN FIBROBLASTS
KAPLAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
KAPLAN, A
ACHORD, DT
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
ACHORD, DT
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
SLY, WS
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1977,
74
(05)
: 2026
-
2030
[10]
HEPATIC RECEPTOR OF AVIAN ORIGIN CAPABLE OF BINDING SPECIFICALLY MODIFIED GLYCOPROTEINS
LUNNEY, J
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
LUNNEY, J
ASHWELL, G
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
ASHWELL, G
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1976,
73
(02)
: 341
-
343
←
1
2
→
共 19 条
[1]
ASHWELL G, 1974, ADV ENZYMOL RAMB, V41, P99
[2]
CHESTER MA, 1977, THESIS LUND, P91
[3]
DENTANDT WR, 1974, J LAB CLIN MED, V83, P403
[4]
TISSUE FRACTIONATION STUDIES .6. INTRACELLULAR DISTRIBUTION PATTERNS OF ENZYMES IN RAT-LIVER TISSUE
DUVE, CD
论文数:
0
引用数:
0
h-index:
0
DUVE, CD
PRESSMAN, BC
论文数:
0
引用数:
0
h-index:
0
PRESSMAN, BC
GIANETTO, R
论文数:
0
引用数:
0
h-index:
0
GIANETTO, R
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
APPELMANS, F
论文数:
0
引用数:
0
h-index:
0
APPELMANS, F
[J].
BIOCHEMICAL JOURNAL,
1955,
60
(1-4)
: 604
-
617
[5]
PHYSICOCHEMICAL MODIFICATIONS OF LYSOSOMAL HYDROLASES DURING INTRACELLULAR TRANSPORT
GOLDSTONE, A
论文数:
0
引用数:
0
h-index:
0
机构:
VET ADM RES HOSP, NEUROL SERV, CHICAGO, IL 60611 USA
GOLDSTONE, A
KOENIG, H
论文数:
0
引用数:
0
h-index:
0
机构:
VET ADM RES HOSP, NEUROL SERV, CHICAGO, IL 60611 USA
KOENIG, H
[J].
BIOCHEMICAL JOURNAL,
1973,
132
(02)
: 267
-
+
[6]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
: 992
-
&
[7]
ROLE OF GLYCOSIDICALLY BOUND MANNOSE IN ASSIMILATION OF BETA-GALACTOSIDASE BY GENERALIZED GANGLIOSIDOSIS FIBROBLASTS
HIEBER, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
HIEBER, V
DISTLER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
DISTLER, J
MYEROWITZ, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
MYEROWITZ, R
SCHMICKEL, RD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
SCHMICKEL, RD
JOURDIAN, GW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
JOURDIAN, GW
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1976,
73
(03)
: 710
-
717
[8]
ARTIFICIAL SUBSTRATES IN ASSAY OF ACID GLYCOSIDASES
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
HULTBERG, B
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
OCKERMAN, PA
[J].
CLINICA CHIMICA ACTA,
1972,
39
(01)
: 49
-
&
[9]
PHOSPHOHEXOSYL COMPONENTS OF A LYSOSOMAL ENZYME ARE RECOGNIZED BY PINOCYTOSIS RECEPTORS ON HUMAN FIBROBLASTS
KAPLAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
KAPLAN, A
ACHORD, DT
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
ACHORD, DT
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, DEPT PEDIAT, DIV MED GENET, ST LOUIS, MO 63110 USA
SLY, WS
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1977,
74
(05)
: 2026
-
2030
[10]
HEPATIC RECEPTOR OF AVIAN ORIGIN CAPABLE OF BINDING SPECIFICALLY MODIFIED GLYCOPROTEINS
LUNNEY, J
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
LUNNEY, J
ASHWELL, G
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
NIAMDD,LAB BIOCHEM & METAB,BETHESDA,MD 20014
ASHWELL, G
[J].
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1976,
73
(02)
: 341
-
343
←
1
2
→