PRIMARY PULMONARY-HYPERTENSION IN ADULTS

被引:2
作者
HAWKINS, JW [1 ]
DUNN, MI [1 ]
机构
[1] UNIV KANSAS,MED CTR,CARDIOVASC DIS SECT,39TH & RAINBOW BLVD,KANSAS CITY,KS 66103
关键词
Primary pulmonary hypertension; pulmonary hypertension; pulmonary vascular disease;
D O I
10.1002/clc.4960130603
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Primary pulmonary hypertension is an enigmatic disease found predominantly in young women, but it also affects a significant number of middle‐aged and elderly males and females. Its onset, characterized by progressively worsening dyspnea, fatigue, and chest pain, is insidious. Three distinct histopathologic subtypes have been identified, and the natural history of the disease process has been well‐defined. Pharmacologic treatment options have, in general, been disappointing, and it appears that heart‐lung transplantation will be applied only to a small minority of young patients with primary pulmonary hypertension in the near future. We review the histopathology, evaluation, treatment, and prognosis of primary pulmonary hypertension. Copyright © 1990 Wiley Periodicals, Inc.
引用
收藏
页码:382 / 387
页数:6
相关论文
共 49 条
[1]   PRIMARY PULMONARY-HYPERTENSION - A HISTOPATHOLOGIC STUDY OF 80 CASES [J].
BJORNSSON, J ;
EDWARDS, WD .
MAYO CLINIC PROCEEDINGS, 1985, 60 (01) :16-25
[2]   MAGNETIC-RESONANCE IMAGING IN PULMONARY ARTERIAL-HYPERTENSION [J].
BOUCHARD, A ;
HIGGINS, CB ;
BYRD, BF ;
AMPARO, EG ;
OSAKI, L ;
AXELROD, R .
AMERICAN JOURNAL OF CARDIOLOGY, 1985, 56 (15) :938-942
[3]   PULMONARY-FUNCTION IN ADVANCED PULMONARY-HYPERTENSION [J].
BURKE, CM ;
GLANVILLE, AR ;
MORRIS, AJR ;
RUBIN, D ;
HARVEY, JA ;
THEODORE, J ;
ROBIN, ED .
THORAX, 1987, 42 (02) :131-135
[4]   DIAGNOSIS OF PULMONARY-HYPERTENSION FROM RADIOGRAPHIC ESTIMATES OF PULMONARY ARTERIAL SIZE [J].
BUSH, A ;
GRAY, H ;
DENISON, DM .
THORAX, 1988, 43 (02) :127-131
[5]   ECHOCARDIOGRAPHIC RECOGNITION OF PULMONARY ARTERIAL-DISEASE AND DETERMINATION OF ITS CAUSE [J].
COME, PC .
AMERICAN JOURNAL OF MEDICINE, 1988, 84 (03) :384-394
[6]   COMPARISON OF PROGRESSIVE EXERCISE PERFORMANCE OF NORMAL SUBJECTS AND PATIENTS WITH PRIMARY PULMONARY-HYPERTENSION [J].
DALONZO, GE ;
POHIL, RL ;
DUREE, SL ;
DANTZKER, DR ;
GIANOTTI, LA .
CHEST, 1987, 92 (01) :57-62
[7]   DIFFERENTIATION OF PATIENTS WITH PRIMARY AND THROMBOEMBOLIC PULMONARY-HYPERTENSION [J].
DALONZO, GE ;
BOWER, JS ;
DANTZKER, DR .
CHEST, 1984, 85 (04) :457-461
[8]   VASODILATORS AND PRIMARY PULMONARY-HYPERTENSION - VARIABILITY OF LONG-TERM RESPONSE [J].
DANTZKER, DR ;
DALONZO, GE ;
GIANOTTI, L ;
FUENTES, F ;
NICKESON, D ;
EMERSON, M .
CHEST, 1989, 95 (06) :1185-1189
[9]   PRIMARY PULMONARY HYPERTENSION .1. CLINICAL AND HEMODYNAMIC STUDY [J].
DRESDALE, DT ;
SCHULTZ, M ;
MICHTOM, RJ .
AMERICAN JOURNAL OF MEDICINE, 1951, 11 (06) :686-705
[10]   CLINICAL PRIMARY PULMONARY-HYPERTENSION - 3 PATHOLOGIC TYPES [J].
EDWARDS, WD ;
EDWARDS, JE .
CIRCULATION, 1977, 56 (05) :884-888