NEUROLOGIC COMPLICATIONS OF NONNEURONOPATHIC GAUCHERS-DISEASE

被引:24
作者
GREWAL, RP
DOPPELT, SH
THOMPSON, MA
KATZ, D
BRADY, RO
BARTON, NW
机构
[1] NINCDS,OFF CLIN DIRECTOR,BETHESDA,MD 20892
[2] NCI,PATHOL LAB,BETHESDA,MD 20892
[3] MASSACHUSETTS GEN HOSP,DEPT ORTHOPED SURG,BOSTON,MA 02114
关键词
D O I
10.1001/archneur.1991.00530240075025
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe eight patients with type 1 Gaucher's disease who developed neurologic complications that were secondary to systemic features of the illness. Four patients experienced neurologic difficulties because of coagulopathy, and the other four patients had involvement of the nervous system secondary to skeletal disease. Early recognition of these complications in patients with type 1 Gaucher's disease may lead to improved neurologic outcome.
引用
收藏
页码:1271 / 1272
页数:2
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