LATE-ONSET GLOBOID-CELL LEUKODYSTROPHY MIMICKING AN INFILTRATING GLIOMA

被引:7
作者
EPSTEIN, MA
ZIMMERMAN, RA
RORKE, LB
SLADKY, JT
机构
[1] UNIV PENN,SCH MED,CHILDRENS HOSP,DEPT NEUROL,PHILADELPHIA,PA 19104
[2] UNIV PENN,SCH MED,CHILDRENS HOSP,DEPT PAEDIAT SURG,PHILADELPHIA,PA 19104
[3] UNIV PENN,SCH MED,CHILDRENS HOSP,DEPT PATHOL,PHILADELPHIA,PA 19104
关键词
D O I
10.1007/BF02015627
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A 3 1/2 year old girl who developed a gradual left hemiparesis and hemianopia is reported. Neuroimaging studies demonstrated an infiltrating-like high density lesion which crossed the splenium of the corpus callosum, though to represent a glioma. Subsequent brain biopsy established the correct diagnosis of globoid cell leukodystrophy (GCL), which suggests that the radiographic appearance of late-onset GCL may mimic that of an infiltrating glioma.
引用
收藏
页码:131 / 132
页数:2
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