DIAGNOSIS AND MANAGEMENT OF LARYNGEAL OBSTRUCTION IN CHILDHOOD PACHYONYCHIA-CONGENITA

被引：10

作者：

WUDY, SA

LENDERS, H

PIRSIG, W

MOHR, W

TELLER, WM

机构：

[1] UNIV ULM,DEPT OTORHINOLARYNGOL,D-89070 ULM,GERMANY

[2] UNIV ULM,DEPT PATHOL,D-89070 ULM,GERMANY

来源：

INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY | 1995年 / 31卷 / 01期

关键词：

PACHYONYCHIA CONGENITA; JADASSOHN-LEWANDOWSKY SYNDROME; LARYNGEAL OBSTRUCTION; HOARSENESS OF VOICE; STRIDOR;

D O I：

10.1016/0165-5876(94)01074-8

中图分类号：

R76 [耳鼻咽喉科学];

学科分类号：

100213 ;

摘要：

Pachyonychia congenita is a genetic syndrome of epithelial dysplasia. In infants and young children, laryngeal involvement can present a life threatening complication: obstruction of the patient's airway due to leukokeratosis can lead to severe respiratory distress. This report concentrates on the diagnosis and successful microsurgical management of laryngeal obstruction in the first female case, a 19-month-old girl with pachyonychia congenita.

引用

页码：109 / 115

页数：7

共 9 条

[1] PACHYONYCHIA CONGENITA WITH INVOLVEMENT OF LARYNX [J].