DOES ORTHOTOPIC LIVER-TRANSPLANTATION HEAL WILSONS-DISEASE - CLINICAL FOLLOW-UP OF 2 LIVER-TRANSPLANTED PATIENTS

被引：24

作者：

HEFTER, H

RAUTENBERG, W

KREUZPAINTNER, G

ARENDT, G

FREUND, HJ

PICHLMAYR, R

STROHMEYER, G

机构：

[1] UNIV DUSSELDORF,DEPT GASTROENTEROL,W-4000 DUSSELDORF 1,GERMANY

[2] UNIV DUSSELDORF,DEPT ABDOMINAL SURG & TRANSPLANTAT,W-4000 DUSSELDORF 1,GERMANY

来源：

ACTA NEUROLOGICA SCANDINAVICA | 1991年 / 84卷 / 03期

关键词：

WILSONS DISEASE; LIVER TRANSPLANTATION; MOTOR IMPAIRMENT; NORMALIZATION OF COPPER METABOLISM;

D O I：

10.1111/j.1600-0404.1991.tb04936.x

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Two patients with Wilson's disease (WD) underwent orthotopic liver transplantation, one for subacute liver failure and the other for severe oesophageal haemorrhage. After transplantation both patients fully recovered within five months, and copper metabolism returned to normal. Follow-up examinations were continued for 4 and 6 years. Clinical as well as electrophysiological testing in these two patients yielded better results than in most of 12 WD-patients being conventionally treated for a similar period or even longer.

引用

页码：192 / 196

页数：5

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