PROTEIN-TURNOVER IN ACID MALTASE DEFICIENCY BEFORE AND AFTER TREATMENT WITH A HIGH PROTEIN-DIET

被引:25
作者
UMPLEBY, AM
WILES, CM
TREND, PS
SCOBIE, IN
MACLEOD, AF
SPENCER, GT
SONKSEN, PH
机构
[1] ST THOMAS HOSP,DEPT NEUROL,LONDON SE1 7EH,ENGLAND
[2] ST THOMAS HOSP,RESP UNIT,LONDON SE1 7EH,ENGLAND
关键词
D O I
10.1136/jnnp.50.5.587
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:587 / 592
页数:6
相关论文
共 19 条
[1]   FREE FATTY-ACID ESTIMATION BY A SEMIAUTOMATED FLUORIMETRIC METHOD [J].
CARRUTHERS, M ;
YOUNG, DAB .
CLINICA CHIMICA ACTA, 1973, 49 (03) :341-348
[2]  
DOLE VP, 1960, J BIOL CHEM, V235, P2595
[3]  
ELIA M, 1981, BRIT MED J, V282, P351, DOI 10.1136/bmj.282.6261.351
[4]   URINARY CREATININE EXCRETION AND LEAN BODY-MASS [J].
FORBES, GB ;
BRUINING, GJ .
AMERICAN JOURNAL OF CLINICAL NUTRITION, 1976, 29 (12) :1359-1366
[5]  
Graystone JE, 1968, HUMAN GROWTH, P182
[6]  
HOHORST HJ, 1959, BIOCHEM Z, V332, P18
[7]   PATHOLOGY OF TYPE-II SKELETAL-MUSCLE GLYCOGENOSIS - LIGHT AND ELECTRON-MICROSCOPIC STUDY [J].
HUDGSON, P ;
FULTHORPE, JJ .
JOURNAL OF PATHOLOGY, 1975, 116 (03) :139-&
[8]   URINARY 3-METHYLHISTIDINE EXCRETION IN JUVENILE-ONSET DIABETICS - EVIDENCE OF INCREASED PROTEIN CATABOLISM IN THE ABSENCE OF KETOACIDOSIS [J].
HUSZAR, G ;
KOIVISTO, V ;
DAVIS, E ;
FELIG, P .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1982, 31 (02) :188-191
[9]  
KAIHARA S, 1968, J LAB CLIN MED, V71, P400
[10]  
KARNI Y, 1984, PHYSIOTHERAPY, V70, P288