IDENTIFICATION OF 15-BETA-HYDROXYLATED C-21 STEROIDS IN THE NEONATAL-PERIOD - THE ROLE OF 3-ALPHA,15-BETA,17-ALPHA-TRIHYDROXY-5-BETA-PREGNAN-20-ONE IN THE PERINATAL DIAGNOSIS OF CONGENITAL ADRENAL-HYPERPLASIA (CAH) DUE TO A 21-HYDROXYLASE DEFICIENCY

被引:39
作者
JOANNOU, GE
机构
关键词
D O I
10.1016/0022-4731(81)90239-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:901 / 912
页数:12
相关论文
共 28 条
[1]   O-BUTYLOXIMES AND O-PENTYLOXIMES AS DERIVATIVES FOR STUDY OF KETOSTEROIDS BY GAS-CHROMATOGRAPHY [J].
BAILLIE, TA ;
BROOKS, CJW ;
HORNING, EC .
ANALYTICAL LETTERS, 1972, 5 (06) :351-&
[2]   C-15 SUBSTITUTED STEROIDS - 15-ALPHA-HYDROXY-REICHSTEIN AND 15-BETA-HYDROXY-REICHSTEIN SUBSTANCE-S AND TRANSFORMATION PRODUCTS [J].
BERNSTEIN, S ;
HELLER, M ;
FELDMAN, LI ;
ALLEN, WS ;
BLANK, RH ;
LINDEN, CE .
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1960, 82 (14) :3685-3689
[3]   CORRELATION OF GAS-LIQUID CHROMATOGRAPHIC BEHAVIOUR AND STRUCTURE OF STEROIDS [J].
BROOKS, CJW ;
HANAINEH, L .
BIOCHEMICAL JOURNAL, 1963, 87 (01) :151-+
[4]   SUBSTRATE SPECIFICITY IN STEROID SIDE-CHAIN DEGRADATION BY MICROORGANISMS [J].
ELTAYEB, O ;
SIH, CJ ;
KNIGHT, SG .
BIOCHIMICA ET BIOPHYSICA ACTA, 1964, 93 (02) :411-&
[5]   EXCRETION OF STEROID HORMONES IN ADULTS - STEROIDS IN URINE FROM A PREGNANT WOMAN [J].
ERIKSSON, H ;
GUSTAFSSON, JA .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1970, 16 (02) :268-+
[6]   ISOLATION OF 15ALPHA-HYDROXYPROGESTERONE FROM HUMAN PREGNANCY URINE [J].
GIANNOPO.G ;
SOLOMON, S .
BIOCHEMISTRY, 1967, 6 (05) :1226-+
[7]   IN-VIVO METABOLISM OF 15ALPHA-HYDROXYPROGESTERONE IN MAN [J].
GIANNOPOULOS, G ;
DURHAM, LJ ;
SOLOMON, S .
BIOCHEMISTRY, 1970, 9 (03) :584-+
[8]   MIGRATIONS OF TRIMETHYLSILYL GROUP UPON ELECTRON IMPACT IN STEROIDS [J].
GUSTAFSS.JA ;
RYHAGE, R ;
SJOVALL, J ;
MORIARTY, RM .
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1969, 91 (05) :1234-&
[9]   STEROIDS IN GERMFREE AND CONVENTIONAL RATS .6. IDENTIFICATION OF 15ALPHA- AND 21-HYDROXYLATED C21 STEROIDS IN FAECES FROM GERMFREE RATS [J].
GUSTAFSSON, JA ;
SJOVALL, J .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1968, 6 (02) :236-+
[10]   CLINICAL APPLICATION OF GAS-CHROMATOGRAPHY ON OPEN TUBULAR GLASS CAPILLARIES .1. DETERMINATION OF URINARY 17-HYDROXYPREGNANOLONE BY GAS CHROMATOGRAPHY-MASS SPECTROMETRY IN PATIENTS WITH CONGENITAL ADRENAL-HYPERPLASIA [J].
HOLSBOER, F ;
KNORR, D .
JOURNAL OF STEROID BIOCHEMISTRY AND MOLECULAR BIOLOGY, 1977, 8 (11) :1197-1199