PATHOGENESIS OF CYSTIC-FIBROSIS

[1] ANDERSON NP, 1992, SCIENCE, V257, P1701

[2] CONGENITAL BILATERAL ABSENCE OF THE VAS-DEFERENS - A PRIMARILY GENITAL FORM OF CYSTIC-FIBROSIS [J]. JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1992, 267 (13): : 1794 - 1797

[3] PURIFICATION AND FUNCTIONAL RECONSTITUTION OF THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) [J]. CELL, 1992, 68 (04) : 809 - 818

[4] BERGER M, 1991, CLIN REV ALLERG, V9, P119

[5] NA+ TRANSPORT IN CYSTIC-FIBROSIS RESPIRATORY EPITHELIA - ABNORMAL BASAL RATE AND RESPONSE TO ADENYLATE-CYCLASE ACTIVATION [J]. JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (05) : 1245 - 1252

[6] EXTENSIVE POSTTRANSCRIPTIONAL DELETION OF THE CODING SEQUENCES FOR PART OF NUCLEOTIDE-BINDING FOLD-1 IN RESPIRATORY EPITHELIAL MESSENGER-RNA TRANSCRIPTS OF THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR GENE IS NOT ASSOCIATED WITH THE CLINICAL MANIFESTATIONS OF CYSTIC-FIBROSIS [J]. JOURNAL OF CLINICAL INVESTIGATION, 1992, 90 (03) : 785 - 790

[7] DEFECTIVE EPITHELIAL CHLORIDE TRANSPORT IN A GENE-TARGETED MOUSE MODEL OF CYSTIC-FIBROSIS [J]. SCIENCE, 1992, 257 (5073) : 1125 - 1128

[8] CFTR - DEVELOPMENT OF HIGH-AFFINITY ANTIBODIES AND LOCALIZATION IN SWEAT GLAND [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1991, 181 (01) : 36 - 43

[9] CYSTIC-FIBROSIS - MOLECULAR-BIOLOGY AND THERAPEUTIC IMPLICATIONS [J]. SCIENCE, 1992, 256 (5058) : 774 - 779

[10] CONG EL, 1989, THORAX, V44, P739

[1] ANDERSON NP, 1992, SCIENCE, V257, P1701

[2] CONGENITAL BILATERAL ABSENCE OF THE VAS-DEFERENS - A PRIMARILY GENITAL FORM OF CYSTIC-FIBROSIS [J]. JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1992, 267 (13): : 1794 - 1797

[3] PURIFICATION AND FUNCTIONAL RECONSTITUTION OF THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) [J]. CELL, 1992, 68 (04) : 809 - 818

[4] BERGER M, 1991, CLIN REV ALLERG, V9, P119

[5] NA+ TRANSPORT IN CYSTIC-FIBROSIS RESPIRATORY EPITHELIA - ABNORMAL BASAL RATE AND RESPONSE TO ADENYLATE-CYCLASE ACTIVATION [J]. JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (05) : 1245 - 1252

[6] EXTENSIVE POSTTRANSCRIPTIONAL DELETION OF THE CODING SEQUENCES FOR PART OF NUCLEOTIDE-BINDING FOLD-1 IN RESPIRATORY EPITHELIAL MESSENGER-RNA TRANSCRIPTS OF THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR GENE IS NOT ASSOCIATED WITH THE CLINICAL MANIFESTATIONS OF CYSTIC-FIBROSIS [J]. JOURNAL OF CLINICAL INVESTIGATION, 1992, 90 (03) : 785 - 790

[7] DEFECTIVE EPITHELIAL CHLORIDE TRANSPORT IN A GENE-TARGETED MOUSE MODEL OF CYSTIC-FIBROSIS [J]. SCIENCE, 1992, 257 (5073) : 1125 - 1128

[8] CFTR - DEVELOPMENT OF HIGH-AFFINITY ANTIBODIES AND LOCALIZATION IN SWEAT GLAND [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1991, 181 (01) : 36 - 43

[9] CYSTIC-FIBROSIS - MOLECULAR-BIOLOGY AND THERAPEUTIC IMPLICATIONS [J]. SCIENCE, 1992, 256 (5058) : 774 - 779

[10] CONG EL, 1989, THORAX, V44, P739