MULTIPLE FORMS OF GLYCOSIDASES IN NORMAL AND PATHOLOGICAL STATES

被引:20
作者
ROBINSON, D [1 ]
机构
[1] QUEEN ELIZABETH COLL, BIOCHEM DEPT, CAMPDEN HILL, LONDON W8 7AH, ENGLAND
关键词
D O I
10.1159/000459418
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:114 / 135
页数:22
相关论文
共 107 条
[1]   BETA-D-GLUCOSIDASES AND RELATED ENZYMIC ACTIVITIES IN PIG KIDNEY [J].
ABRAHAMS, HE ;
ROBINSON, D .
BIOCHEMICAL JOURNAL, 1969, 111 (05) :749-&
[2]   URINARY AMINO-ACID OUTPUT IN CHILDREN WITH HURLERS SYNDROME [J].
APPLEGARTH, DA ;
BOZOIAN, G ;
STURROCK, S ;
TISCHLER, B .
CLINICA CHIMICA ACTA, 1972, 39 (01) :258-+
[3]   PURIFICATION OF AN ACID ALPHA-GLUCOSIDASE BY DEXTRAN-GEL FILTRATION [J].
AURICCHIO, F ;
BRUNI, CB .
BIOCHEMICAL JOURNAL, 1967, 105 (01) :35-+
[4]   DEXTRAN-GEL FILTRATION OF RAT LIVER ALPHA-GLUCOSIDASES [J].
AURICCHIO, F ;
SICA, V .
JOURNAL OF CHROMATOGRAPHY, 1967, 28 (01) :26-+
[5]  
AURICCHIO S, 1963, BIOCHIM BIOPHYS ACTA, V73, P582
[6]   DEFECT IN HURLER AND SCHEIE SYNDROMES - DEFICIENCY OF ALPHA-IDURONIDASE [J].
BACH, G ;
WEISSMAN.B ;
FRIEDMAN, R ;
NEUFELD, EF .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (08) :2048-&
[7]   FABRYS DISEASE AS AN ALPHA-GALACTOSIDOSIS - EVIDENCE FOR AN ALPHA-CONFIGURATION IN TRIHEXOSYL CERAMIDE [J].
BENSAUDE, I ;
CALLAHAN, J ;
PHILIPPART, M .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1971, 43 (04) :913-+
[8]  
BEUTLER E, 1972, AM J HUM GENET, V24, P237
[9]   RELATIONSHIP BETWEEN HUMAN ALPHA-GALACTOSIDASE ISOENZYMES [J].
BEUTLER, E ;
KUHL, W .
NATURE-NEW BIOLOGY, 1972, 239 (94) :207-&
[10]   PROPERTIES OF CEREBROSIDE GALACTOSIDASE [J].
BOWEN, DM ;
RADIN, NS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 152 (03) :599-&