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ENZYMATIC DEFECT IN VARIEGATE PORPHYRIA - STUDIES WITH HUMAN CULTURED SKIN FIBROBLASTS
被引:159
作者
:
BRENNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520
YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520
BRENNER, DA
[
1
]
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520
YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520
BLOOMER, JR
[
1
]
机构
:
[1]
YALE UNIV,SCH MED,HOWARD HUGHES MED INST LAB,NEW HAVEN,CT 06520
来源
:
NEW ENGLAND JOURNAL OF MEDICINE
|
1980年
/ 302卷
/ 14期
关键词
:
D O I
:
10.1056/NEJM198004033021401
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:765 / 769
页数:5
相关论文
共 26 条
[1]
REDUCED FERROCHELATASE ACTIVITY - DEFECT COMMON TO PORPHYRIA VARIEGATA AND PROTOPORPHYRIA
BECKER, DM
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
BECKER, DM
VILJOEN, JD
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
VILJOEN, JD
KATZ, J
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
KATZ, J
KRAMER, S
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
KRAMER, S
[J].
BRITISH JOURNAL OF HAEMATOLOGY,
1977,
36
(02)
: 171
-
179
[2]
BLOOMER JR, 1976, LANCET, V2, P226
[3]
STUDY OF FACTORS CAUSING EXCESS PROTOPORPHYRIN ACCUMULATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH PROTOPORPHYRIA
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
BLOOMER, JR
BRENNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
BRENNER, DA
MAHONEY, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
MAHONEY, MJ
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1977,
60
(06)
: 1354
-
1361
[4]
BONKOWSKY HL, 1975, J LAB CLIN MED, V85, P93
[5]
HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA - DEMONSTRATION OF DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS
BONKOWSKY, HL
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
BONKOWSKY, HL
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
BLOOMER, JR
EBERT, PS
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
EBERT, PS
MAHONEY, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
MAHONEY, MJ
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1975,
56
(05)
: 1139
-
1148
[6]
BOTTOMLEY SS, 1975, J LAB CLIN MED, V86, P126
[7]
FLUOROMETRIC ASSAY FOR MEASUREMENT OF PROTOPORPHYRINOGEN OXIDASE ACTIVITY IN MAMMALIAN TISSUE
BRENNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
BRENNER, DA
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
BLOOMER, JR
[J].
CLINICA CHIMICA ACTA,
1980,
100
(03)
: 259
-
266
[8]
BRODIE MJ, 1977, LANCET, V2, P699
[9]
ELDER GH, 1976, LANCET, V2, P1217
[10]
RED-CELL UROPORPHYRINOGEN DECARBOXYLASE ACTIVITY IN PORPHYRIA CUTANEA-TARDA AND IN OTHER FORMS OF PORPHYRIA
FELSHER, BF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
FELSHER, BF
NORRIS, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
NORRIS, ME
SHIH, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
SHIH, JC
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1978,
299
(20)
: 1095
-
1098
←
1
2
3
→
共 26 条
[1]
REDUCED FERROCHELATASE ACTIVITY - DEFECT COMMON TO PORPHYRIA VARIEGATA AND PROTOPORPHYRIA
BECKER, DM
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
BECKER, DM
VILJOEN, JD
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
VILJOEN, JD
KATZ, J
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
KATZ, J
KRAMER, S
论文数:
0
引用数:
0
h-index:
0
机构:
S AFRICAN INST MED RES,DEPT HAEMATOL,JOHANNESBURG 2000,SOUTH AFRICA
KRAMER, S
[J].
BRITISH JOURNAL OF HAEMATOLOGY,
1977,
36
(02)
: 171
-
179
[2]
BLOOMER JR, 1976, LANCET, V2, P226
[3]
STUDY OF FACTORS CAUSING EXCESS PROTOPORPHYRIN ACCUMULATION IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH PROTOPORPHYRIA
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
BLOOMER, JR
BRENNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
BRENNER, DA
MAHONEY, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV,SCH MED,DEPT MED,NEW HAVEN,CT 06510
MAHONEY, MJ
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1977,
60
(06)
: 1354
-
1361
[4]
BONKOWSKY HL, 1975, J LAB CLIN MED, V85, P93
[5]
HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA - DEMONSTRATION OF DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS
BONKOWSKY, HL
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
BONKOWSKY, HL
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
BLOOMER, JR
EBERT, PS
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
EBERT, PS
MAHONEY, MJ
论文数:
0
引用数:
0
h-index:
0
机构:
DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001
MAHONEY, MJ
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1975,
56
(05)
: 1139
-
1148
[6]
BOTTOMLEY SS, 1975, J LAB CLIN MED, V86, P126
[7]
FLUOROMETRIC ASSAY FOR MEASUREMENT OF PROTOPORPHYRINOGEN OXIDASE ACTIVITY IN MAMMALIAN TISSUE
BRENNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
BRENNER, DA
BLOOMER, JR
论文数:
0
引用数:
0
h-index:
0
机构:
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
YALE UNIV, SCH MED, HOWARD HUGHES MED INST LAB, NEW HAVEN, CT 06520 USA
BLOOMER, JR
[J].
CLINICA CHIMICA ACTA,
1980,
100
(03)
: 259
-
266
[8]
BRODIE MJ, 1977, LANCET, V2, P699
[9]
ELDER GH, 1976, LANCET, V2, P1217
[10]
RED-CELL UROPORPHYRINOGEN DECARBOXYLASE ACTIVITY IN PORPHYRIA CUTANEA-TARDA AND IN OTHER FORMS OF PORPHYRIA
FELSHER, BF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
FELSHER, BF
NORRIS, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
NORRIS, ME
SHIH, JC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
UNIV CALIF IRVINE,SCH MED,IRVINE,CA 92664
SHIH, JC
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1978,
299
(20)
: 1095
-
1098
←
1
2
3
→