PROPRIOSPINAL MYOCLONUS - EVIDENCE FOR SPINAL PATTERN GENERATORS IN HUMANS

被引:94
作者
BROWN, P [1 ]
ROTHWELL, JC [1 ]
THOMPSON, PD [1 ]
MARSDEN, CD [1 ]
机构
[1] UNIV LONDON,NATL HOSP NEUROL & NEUROSURG,DEPT CLIN NEUROL,LONDON,ENGLAND
关键词
PROPRIOSPINAL MYOCLONUS; SPINAL PATTERN GENERATOR;
D O I
10.1002/mds.870090511
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The clinical and electrophysiological characteristics of eight patients with propriospinal myoclonus are described. Myoclonus developed within days or weeks of cervical trauma in half the patients. Seven cases had axial flexion jerks, and one axial extension jerks. Myoclonic EMG activity consisted of repetitive bursts with a frequency of 1-7 Hz. The jerks in three of the cases were comprised of alternating and rhythmic bursts of EMG activity in rectus abdominis and the paraspinal muscles. From these new observations, it is proposed that cervical trauma can lead to the partial release of a spinal pattern generator. The latter is capable of recruiting muscles through long propriospinal pathways into complex rhythmic activity.
引用
收藏
页码:571 / 576
页数:6
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