ABNORMAL PROCOLLAGEN SYNTHESIS IN FIBROBLASTS FROM THREE PATIENTS OF THE SAME FAMILY WITH A SEVERE FORM OF OSTEOGENESIS IMPERFECTA (TYPE-III)

被引：13

作者：

BONAVENTURE, J ^{[1
]}

COHENSOLAL, L ^{[1
]}

LASSELIN, C ^{[1
]}

ALLAIN, JC ^{[1
]}

MAROTEAUX, P ^{[1
]}

机构：

[1] HOP NECKER ENFANTS MALAD,CNRS,VA 584,F-75743 PARIS 15,FRANCE

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1986年 / 889卷 / 01期

关键词：

D O I：

10.1016/0167-4889(86)90005-4

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：23 / 34

页数：12

共 37 条

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[20] A DEFECT IN THE STRUCTURE OF TYPE-I PROCOLLAGEN IN A PATIENT WHO HAD OSTEOGENESIS IMPERFECTA - EXCESS MANNOSE IN THE COOH-TERMINAL PROPEPTIDE [J].

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