ADRENOCORTICOTROPIC HORMONE-SECRETING GANGLIONEUROBLASTOMA ASSOCIATED WITH OPSOMYOCLONIC ENCEPHALOPATHY - A CASE-REPORT WITH IMMUNOHISTOCHEMICAL STUDY

被引:11
作者
CLERICO, A
TENORE, A
BARTOLOZZI, S
REMOTTI, D
RUCO, L
DOMINICI, C
PROPERZI, E
CASTELLO, MA
机构
[1] UNIV ROMA LA SAPIENZA,DEPT PEDIAT,I-00185 ROME,ITALY
[2] UNIV ROMA LA SAPIENZA,DEPT HUMAN BIOPATHOL,SERV IMMUNOPATHOL,I-00185 ROME,ITALY
[3] UNIV NAPLES,DEPT PEDIAT,I-80138 NAPLES,ITALY
来源
MEDICAL AND PEDIATRIC ONCOLOGY | 1993年 / 21卷 / 09期
关键词
CEREBELLAR LESIONS; CUSHINGS SYNDROME; IMMUNOHISTOCHEMISTRY;
D O I
10.1002/mpo.2950210916
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
This report describes a case of a 3-year-old female with Cushing's syndrome associated with ganglioneuroblastoma and opsomyoclonic encephalopathy. Immunohistochemistry showed the tumor to be adrenocorticotropic hormone-secreting. At autopsy, a cerebellar degenerative lesion was also demonstrated. (C) 1993 Wiley-Liss, Inc.
引用
收藏
页码:690 / 694
页数:5
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