OPTICAL ROTATORY DISPERSION OF MUCOPOLYSACCHARIDES .4. OPTICAL ROTATORY DISPERSION AND CIRCULAR DICHROISM OF GLYCOSAMINOGLYCANS AND HEPARAN SULFATE FRACTIONS FROM URINE OF PATIENTS WITH MUCOPOLYSACCHARIDOSIS (HURLER-SYNDROME)

被引:18
作者
STONE, AL
CONSTANTOPOULOS, G
SOTSKY, SM
DEKABAN, A
机构
关键词
D O I
10.1016/0304-4165(70)90353-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:79 / +
页数:1
相关论文
共 21 条
[1]  
CIFONELLI JA, 1960, J BIOL CHEM, V235, P3283
[2]  
CIFONELLI JA, 1964, FED PROC, V23, P484
[3]  
CIFONELLI JA, CHEMISTRY MOLECULAR, V2, P961
[4]   HUNTER-HURLER SYNDROME - GEL FILTRATION AND DIALYSIS OF URINARY ACID MUCOPOLYSACCHARIDES [J].
CONSTANTOPOULOS, G .
NATURE, 1968, 220 (5167) :583-+
[5]   DETERMINATION OF MOLECULAR WEIGHT DISTRIBUTION OF ACID MUCOPOLYSACCHARIDES BY SEPHADEX GEL FILTRATION [J].
CONSTANTOPOULOS, G ;
DEKABAN, AS ;
CARROLL, WR .
ANALYTICAL BIOCHEMISTRY, 1969, 31 (1-3) :59-+
[6]  
FARBER S, IN PRESS
[7]   DEFECT IN HURLERS AND HUNTERS SYNDROMES - FAULTY DEGRADATION OF MUCOPOLYSACCHARIDE [J].
FRATANTONI, JC ;
HALL, CW ;
NEUFELD, EF .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1968, 60 (02) :699-+
[8]  
KNECHT J, 1967, J BIOL CHEM, V242, P4652
[9]   STRUCTURE OF HEPARITIN SULFATE IN TISSUES OF HURLER SYNDROME [J].
KNECHT, J ;
DORFMAN, A .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1965, 21 (05) :509-&
[10]   HEPARITIN SULFATE [J].
LINKER, A ;
HOFFMAN, P ;
SAMPSON, P ;
MEYER, K .
BIOCHIMICA ET BIOPHYSICA ACTA, 1958, 29 (02) :443-444