MOLECULAR-GENETICS OF THE CUTANEOUS BASEMENT-MEMBRANE ZONE - PERSPECTIVES ON EPIDERMOLYSIS-BULLOSA AND OTHER BLISTERING SKIN DISEASES

被引:153
作者
UITTO, J [1 ]
CHRISTIANO, AM [1 ]
机构
[1] THOMAS JEFFERSON UNIV,JEFFERSON MED COLL,JEFFERSON INST MOLEC MED,DEPT BIOCHEM & MOLEC BIOL SECT,PHILADELPHIA,PA 19107
关键词
D O I
10.1172/JCI115938
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
[No abstract available]
引用
收藏
页码:687 / 692
页数:6
相关论文
共 43 条
[1]   AUTOANTIBODIES AGAINST THE AMINO-TERMINAL CADHERIN-LIKE BINDING DOMAIN OF PEMPHIGUS-VULGARIS ANTIGEN ARE PATHOGENIC [J].
AMAGAI, M ;
KARPATI, S ;
PRUSSICK, R ;
KLAUSKOVTUN, V ;
STANLEY, JR .
JOURNAL OF CLINICAL INVESTIGATION, 1992, 90 (03) :919-926
[2]  
ARNEMANN J, 1992, HUM GENET, V89, P347
[3]  
BACHINGER HP, 1990, J BIOL CHEM, V265, P10095
[4]  
BAUER EA, 1984, ANN NY ACAD SCI, V460, P311
[5]   EPIDERMOLYSIS-BULLOSA SIMPLEX - EVIDENCE IN 2 FAMILIES FOR KERATIN GENE ABNORMALITIES [J].
BONIFAS, JM ;
ROTHMAN, AL ;
EPSTEIN, EH .
SCIENCE, 1991, 254 (5035) :1202-1205
[6]  
BRUCKNERTUDERMAN L, 1991, EUR J DERMATOL, V1, P89
[7]   THE STRUCTURE AND FUNCTION OF TYPE-VII COLLAGEN [J].
BURGESON, RE ;
LUNSTRUM, GP ;
ROKOSOVA, B ;
RIMBERG, CS ;
ROSENBAUM, LM ;
KEENE, DR .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1990, 580 :32-43
[8]   TREATMENT OF JUNCTIONAL EPIDERMOLYSIS-BULLOSA WITH EPIDERMAL AUTOGRAFTS [J].
CARTER, DM ;
LIN, AN ;
VARGHESE, MC ;
CALDWELL, D ;
PRATT, LA ;
EISINGER, M .
JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1987, 17 (02) :246-250
[9]   EPILIGRIN, A NEW CELL-ADHESION LIGAND FOR INTEGRIN ALPHA-3-BETA-1 IN EPITHELIAL BASEMENT-MEMBRANES [J].
CARTER, WG ;
RYAN, MC ;
GAHR, PJ .
CELL, 1991, 65 (04) :599-610
[10]  
CHRISTIANO A M, 1992, Journal of Investigative Dermatology, V98, P552