DYSPLASIA OF THE KIDNEYS, LIVER, AND PANCREAS - REPORT OF A VARIANT OF IVEMARKS SYNDROME

被引:18
作者
STRAYER, DS [1 ]
KISSANE, JM [1 ]
机构
[1] BARNES HOSP,ST LOUIS,MO 63110
关键词
D O I
10.1016/S0046-8177(79)80011-8
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
A newborn girl with respiratory distress due to bilateral pneumothorax was found to be anuric, and died at 18 hours of age. Autopsy revealed a large pancreatic cyst, multiple large hepatic cysts, congenital hepatic fibrosis, bilateral dysplastic kidneys, and dysplasia of the pancreas. These findings constitute a variant of Ivemark's syndrome of dysplasia of the pancreas, liver, and kidneys. © 1979 W. B. Saunders Company.
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页码:228 / 234
页数:7
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