DIFFUSE NEONATAL HEMANGIOMATOSIS - A NEW CONSTELLATION OF FINDINGS

被引:32
作者
GELLER, JD
TOPPER, SF
HASHIMOTO, K
机构
[1] Detroit, Michigan
关键词
D O I
10.1016/0190-9622(91)70121-H
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Diffuse neonatal hemangiomatosis is a rare, frequently fatal disease characterized by multiple cutaneous and visceral hemangiomas. The skin, liver, lungs, intestines, and central nervous system are the most commonly affected organs. Death can result from high-output cardiac failure as a result of arteriovenous shunting. In this report we present a new constellation of findings in a patient with diffuse neonatal hemangiomatosis, namely, an absent corpus callosum, ectopia cordis (sternal agenesis) with median abdominal raphe, and tricuspid atresia.
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页码:816 / 818
页数:3
相关论文
共 18 条
[1]  
BRUCHANOW N, 1899, Z HEILK, V20, P131
[2]   DISSEMINATED HEMANGIOMATOSIS - NEWBORN WITH CENTRAL NERVOUS SYSTEM INVOLVEMENT [J].
BURKE, EC ;
STRICKLAND, MK ;
WINKELMANN, RK .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1964, 108 (04) :418-+
[3]   MILIARY HAEMANGIOMATA IN NEWBORN [J].
BURMAN, D ;
MANSELL, PWA ;
WARIN, RP .
ARCHIVES OF DISEASE IN CHILDHOOD, 1967, 42 (222) :193-&
[4]  
COOPER AG, 1965, PEDIATRICS, V35, P27
[5]  
Golitz L E, 1986, Pediatr Dermatol, V3, P145, DOI 10.1111/j.1525-1470.1986.tb00506.x
[6]   STERNAL MALFORMATION VASCULAR DYSPLASIA ASSOCIATION [J].
HERSH, JH ;
WATERFILL, D ;
RUTLEDGE, J ;
HARROD, MJE ;
OSHEAL, SF ;
VERDI, G ;
MARTINEZ, S ;
WEISSKOPF, B .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1985, 21 (01) :177-186
[7]  
HOLDEN KR, 1970, PEDIATRICS, V46, P411
[8]  
Jaffe RH, 1929, ARCH PATHOL, V7, P44
[9]  
KELLER L, 1979, CUTIS, V23, P295
[10]  
MCLEAN RH, 1972, PEDIATRICS, V49, P563