POLYSPLENIA WITH PULMONARY ARTERIOVENOUS-MALFORMATIONS

被引：35

作者：

PAPAGIANNIS, J

KANTER, RJ

EFFMAN, EL

PRATT, PC

MARCILLE, R

BROWNING, IB

ARMSTRONG, BE

机构：

[1] DUKE UNIV,MED CTR,DEPT PEDIAT,DIV PEDIAT CARDIOL,POB 3195,DURHAM,NC 27710

[2] DUKE UNIV,MED CTR,DEPT PATHOL,DURHAM,NC 27710

[3] DUKE UNIV,MED CTR,DEPT PEDIAT,DIV PEDIAT PULM MED,DURHAM,NC 27710

[4] DUKE UNIV,MED CTR,DEPT PEDIAT,DIV PEDIAT RADIOL,DURHAM,NC 27710

来源：

PEDIATRIC CARDIOLOGY | 1993年 / 14卷 / 02期

关键词：

POLYSPLENIA; PULMONARY ARTERIOVENOUS MALFORMATIONS; PORTOSYSTEMIC ANASTOMOSIS;

D O I：

10.1007/BF00796995

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A patient with polysplenia syndrome, dextrocardia, left atrial isomerism, normal great vessel relationships, and no intracardiac shunts developed progressive cyanosis and clubbing. Pulmonary arteriovenous malformations (PAVMs) were diagnosed by angiography and confirmed by lung biopsy. Superior mesenteric arteriogram revealed hypoplasia of the intrahepatic portal vein branches and a portosystemic shunt. The possible etiologies of PAVMs are discussed.

引用

页码：127 / 129

页数：3

共 11 条

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