IMMUNOCYTOCHEMICAL STUDY OF NEBULIN IN DUCHENNE MUSCULAR-DYSTROPHY

被引:19
作者
BONILLA, E
MIRANDA, AF
PRELLE, A
SALVIATI, G
BETTO, R
ZEVIANI, M
SCHON, EA
DIMAURO, S
ROWLAND, LP
机构
[1] COLUMBIA PRESBYTERIAN MED CTR,H HOUSTON MERRITT CLIN RES CTR MUSCULAR DYSTROPHY & RELATED DIS,NEW YORK,NY 10032
[2] UNIV PADUA,CNR,MUSCLE BIOL & PHYSIOPATHOL UNIT,I-35100 PADUA,ITALY
关键词
D O I
10.1212/WNL.38.10.1600
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1600 / 1603
页数:4
相关论文
共 17 条
  • [1] BUSH WA, 1972, J CELL BIOL, V52, P367
  • [2] NEBULIN AND TITIN EXPRESSION IN DUCHENNE MUSCULAR-DYSTROPHY APPEARS NORMAL
    FURST, D
    NAVE, R
    OSBORN, M
    WEBER, K
    BARDOSI, A
    ARCHIDIACONO, N
    FERRO, M
    ROMANO, V
    ROMEO, G
    [J]. FEBS LETTERS, 1987, 224 (01) : 49 - 53
  • [3] DYSTROPHIN - THE PROTEIN PRODUCT OF THE DUCHENNE MUSCULAR-DYSTROPHY LOCUS
    HOFFMAN, EP
    BROWN, RH
    KUNKEL, LM
    [J]. CELL, 1987, 51 (06) : 919 - 928
  • [4] SUBCELLULAR FRACTIONATION OF DYSTROPHIN TO THE TRIADS OF SKELETAL-MUSCLE
    HOFFMAN, EP
    KNUDSON, CM
    CAMPBELL, KP
    KUNKEL, LM
    [J]. NATURE, 1987, 330 (6150) : 754 - 758
  • [5] DIFFERENT MUSCLE-SPECIFIC FORMS OF RABBIT SKELETAL-MUSCLE ALPHA-ACTININ
    KOBAYASHI, R
    ITOH, H
    TASHIMA, Y
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1984, 143 (01): : 125 - 131
  • [6] MEDORI R, 1987, J NEUROPATHOL EXP NE, V46, P35
  • [7] MIRANDA A F, 1987, Journal of Cell Biology, V105, p27A
  • [8] MONACO AP, 1986, NATURE, V323, P644
  • [9] THE PRESENCE OF 2 SKELETAL-MUSCLE ALPHA-ACTININS CORRELATES WITH TROPONIN TROPOMYOSIN EXPRESSION AND Z-LINE WIDTH
    SCHACHAT, FH
    CANINE, AC
    BRIGGS, MM
    REEDY, MC
    [J]. JOURNAL OF CELL BIOLOGY, 1985, 101 (03) : 1001 - 1008
  • [10] IS NEBULIN THE PRODUCT OF DUCHENNE MUSCULAR-DYSTROPHY GENE
    SUGITA, H
    NONAKA, I
    ITOH, Y
    ASAKURA, A
    HU, DH
    KIMURA, S
    MARUYAMA, K
    [J]. PROCEEDINGS OF THE JAPAN ACADEMY SERIES B-PHYSICAL AND BIOLOGICAL SCIENCES, 1987, 63 (03): : 107 - 110