ASSOCIATION OF JUVENILE AND ADENOMATOUS POLYPOSIS WITH PULMONARY ARTERIOVENOUS MALFORMATION AND HYPERTROPHIC OSTEOARTHROPATHY

The juvenile form is the usual type of colonic polyp seen during childhood. However, mixed forms associating juvenile and adenomatous polyps have been reported. A syndrome including the association of generalized juvenile polyposis, pulmonary arteriovenous malformation, and hypertrophic osteoarthropathy has been The case reported here is a nonfamilial variant of the syndrome described by Cox et al., and it is also described in three cases; however, this is the first report of the association of mixed juvenile and adenomatous polyposis, pulmonary arteriovenous malformation, and hypertrophic osteoarthropathy. © 1990 Raven Press, Ltd., New York.