THE SPONDYLOMETAPHYSEAL DYSPLASIAS - A TENTATIVE CLASSIFICATION

被引:37
作者
MAROTEAUX, P
SPRANGER, J
机构
[1] HOP NECKER ENFANTS MALAD, CNRS, URA 584, 149 RUE SEVRES, F-75743 PARIS 15, FRANCE
[2] UNIV MAINZ, KINDER KLIN MAINZ, W-6500 MAINZ, GERMANY
关键词
D O I
10.1007/BF02018629
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The spondylometaphyseal dysplasias constitute a very complex group of disorders. In addition to the Kozlowski type, three subgroups can be distinguished by the appearance of the femoral neck. In the first group (A) the changes are severe with absent ossification of the femoral neck and coxa vara. In the second group (B) the changes of the femoral neck are moderate and in the third (C) mild metaphyseal irregularities are only visible. This classification is not definitive but tries to put order in this confusing section of constitutional bone diseases.
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页码:293 / 297
页数:5
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